Susac syndrome

(redirected from Susac's syndrome)
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Susac syndrome

(soo'sak?)
[John O. Susac, U.S. neurologist, 1941–2012]
A rare vascular disease characterized by acute encephalopathy, branched retinal artery occlusion, and sensorineural hearing loss. It typically afflicts teenage girls.
Synonym: retinocochleocerebral vasculopathy
Medical Dictionary, © 2009 Farlex and Partners
References in periodicals archive ?
Susac's Syndrome. Susac's syndrome (SS) is a rare immune disease characterized by encephalopathy, branch retinal artery occlusion, and SNHL [98].
Gevatosky, 27, of Eugene has Susac's syndrome, a rare autoimmune disease that affects about one in 1 million people, according to neuro-ophthalmologist Robert Egan.
It incorporates other entities, such as familial high density lipoprotein deficiency syndromes, Sanjad-Sakati syndrome/Kenny-Caffey syndrome type 1, Loeys-Dietz syndrome, immune recovery uveitis, ectrodactyl-ectodermal dysplasia, trichothiodystrophy, PTEN (phosphatase and tensin homolog) hamartoma tumor syndrome, Susac's syndrome, autosomal dominant occult macular dystrophy, Tolosa-Hunt syndrome, KEttner tumor, caliber persistent artery, solitary circumscribed retina astrocytic proliferation, progressive transformation of germinal centers, and others.
Susac's syndrome is another micro-angiopathy that can present with WMD in adults in their 3rd to 5th decades of life.