Steinert, Hans

(redirected from Steinert myotonic dystrophy)


(Steinhert), Hans, German physician, 1875–.
Curschmann-Batten-Steinert syndrome - see under Curschmann
Steinert disease - a chronic, slowly progressing disease marked by atrophy of the muscles, failing vision, lenticular opacities, ptosis, slurred speech, and general muscular weakness. Synonym(s): myotonic dystrophy
Steinert myotonic dystrophy
Steinert syndrome
References in periodicals archive ?
Steinert myotonic dystrophy is classified into 2 types: muscular dystrophy type 1 (MD1) or classical muscular dystrophy (Steinert disease) of congenital nature due to alteration of the transcription of the genes encoding for chloride channels, insulin receptors, troponins, and N-methyl De Aspartate (NMDA) receptors.
(3,41) In case of dystrophies affecting the heart, such as Steinert myotonic dystrophy, Emery--Dreifus, and limb-girdle, the patients will require anesthesia for implanting cardio defibrillators and pacemakers (1,30,31,36,42) because of the high risk of sudden death caused by ventricular fibrillation, ventricular tachycardia, or complete heart block (26); in advanced stages, patients require tracheostomies, gastrostomies, and therapeutic or diagnostic procedures such as computarized tomography-scans and magnetic resonance image.