Rapunzel syndrome


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A fanciful term for the symptoms of a massive trichobezoar caused by trichotillomania and trichophagia, which occurs mainly in female psychiatric or mentally retarded patients
Imaging Mass lesion, usually gastric with ‘strands’ of hair extending into upper small intestine
Lab Hypochromic microcytic anaemia—hair chelates iron
Management Surgery

Rapunzel syndrome

A fanciful term for the Sx of a massive trichobezoar caused by trichotillomania and trichophagia, seen mainly in mentally retarded or deranged ♀ Clinical Epigastric pain, bloating, N&V Radiology Mass lesion, usually gastric with 'strands' of hair extending into upper small intestine Lab Hypochromic microcytic anemia–hair is an iron chelator Treatment Surgery. See Bezoar.

Rapunzel syndrome

(ră-pŭn′zĕl) [ Rapunzel, a long-haired girl in a fairy tale by the Brothers Grimm]
The extension of a hairball into the small intestine, causing obstruction of the small or large bowel.

Rapunzel,

legendary young woman whose long hair allowed her to escape from a tower in which she was held captive.
Rapunzel syndrome - internal matter that has formed a compact body that occasionally assumes the appearance of strands of twisted hair that extend from a bezoar through the intestine. Synonym(s): bezoar
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References in periodicals archive ?
We report the case of a young girl with Rapunzel syndrome that presented with an epigastric mass and focal alopecia.
Various criteria have been used in the literature to define Rapunzel syndrome: a gastric trichobezoar with a tail extending up to the ileocaecal junction, [11] a simple trichobezoar with a long tail extending beyond the pylorus, [2] or a bezoar of any size causing obstruction.
Naik et al., "Rapunzel syndrome reviewed and redefined," Digestive Surgery, vol.
Rapunzel syndrome causing gastric emphysema and small bowel obstruction.
Trichobezoar, Rapunzel syndrome, Tricho-plaster bezoar--a report of three cases.
Swain first described trichobezoar while conducting an autopsy in 1854.8 Once the bezoar extends from the stomach into the jejunum or further on, it is referred to as "Rapunzel syndrome," which was first described in 1968 by Vaughan Jr.
(8, 9) When the trichobezoar is seen extending from the stomach to various lengths of the intestine is called "Rapunzel Syndrome", for its resemblance to a tail.
An unusual case of gastric perforation in childhood: trichobezoar (Rapunzel syndrome).
The Rapunzel syndrome is a rare clinical entity where a long tail of hair strands from the gastric trichobezoar extends along the small bowel to reach the caecum and beyond.
Gastric trichobezoar with a long intestinal tail is known as Rapunzel syndrome, after the Grimm brothers' story in which the prince climbed into Rapunzel's tower using the tresses of her long hair.