As it became harder for him to use a gastric tube, the Disney fan and Jurassic World enthusiast was diagnosed with complete gut failure and a condition called intestinal pseudoobstruction
Assessment and outcome of pediatric intestinal pseudoobstruction
(PIPO): A tertiary care center experience from Turkey
Deletion of Pten in the mouse enteric nervous system induces ganglioneuromatosis and mimics intestinal pseudoobstruction
. J Clin Invest.
With regard to imaging, 38 cases of pseudoobstruction
(77%) were identified by plain radiograph, ultrasonography, and CT.
The fourth control was later diagnosed with pseudoobstruction
and has still an ileostomy.
The acute colonic pseudoobstruction
(ACPO), nonobstructive colonic dilatation, or Ogilvie's syndrome is a rare entity that is characterized by acute dilatation of the colon, usually involving caecum and right hemicolon in the absence of any mechanical obstruction (80-90%), abdominal pain (80%), abdominal tenderness (62%), nausea and/or vomiting (60%), constipation (40%), and fever (37%).
Diffuse gastrointestinal motility disorders, such as chronic intestinal pseudoobstruction
(CIPO), scleroderma, and hollow visceral myopathy syndrome, can also warrant a MVTx [12, 33].
Multiple phenotypes of ACTG2 related disorders have been described including megacystis microcolon intestinal hypoperistalsis syndrome (MMIHS), prune belly sequence, and chronic intestinal pseudoobstruction
Chronic intestinal pseudoobstruction
can also present as surgical emergency.
Robbie has myopathic pseudoobstruction
- a rare condition that destroys the digestive system leaving him unable to eat normally.
Syndrome, Gastroparesis, GERD, Achalasia
Other intestinal complications such as megacolon (mostly asymptomatic), pseudoobstruction
, sigmoid volvulus, and bowel perforation may also arise in severe conditions, although their exact incidence is still currently unknown [32, 37, 38, 48].