Erdheim-Chester disease

(redirected from Polyostotic sclerosing histiocytosis)

Erd·heim-Chester disease

(erd'hīm-ches'tĕr),
rare systemic disorder characterized by proliferation of histocytes, by symmetric sclerosis at diametaphysial portions of lower limbs, and by extraskeletal involvement. Microscopically, infiltration of affected organs by lipophages and Touton giant cells is evident.
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References in periodicals archive ?
Polyostotic sclerosing histiocytosis, also known as Erdheim-Chester disease (ECD), is a rare form of non-Langerhans histiocytosis.
Williams, "Case report: Erdheim-Chester disease: polyostotic sclerosing histiocytosis," Clinical Radiology, vol.