Erdheim-Chester disease

(redirected from Polyostotic sclerosing histiocytosis)

Erd·heim-Chester disease

rare systemic disorder characterized by proliferation of histocytes, by symmetric sclerosis at diametaphysial portions of lower limbs, and by extraskeletal involvement. Microscopically, infiltration of affected organs by lipophages and Touton giant cells is evident.
Farlex Partner Medical Dictionary © Farlex 2012
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Polyostotic sclerosing histiocytosis, also known as Erdheim-Chester disease (ECD), is a rare form of non-Langerhans histiocytosis.
Williams, "Case report: Erdheim-Chester disease: polyostotic sclerosing histiocytosis," Clinical Radiology, vol.