PEComa

PEComa

A group of mesenchymal tumors composed of epithelioid and spindle cells displaying perivascular epithelioid (PEC) differentiation. The PEComa family of tumors includes angiomyolipoma, clear-cell "sugar" tumor of lung and gastrointestinal tract and other sites, lymphangioleimyomatosis, clear-cell myomelanocytic tumor of the falciform ligament.

PEComa

A rare, possibly mesenchymal tumour of unknown origin and of uncertain malignant potential, which can arise anywhere in the body and more commonly affects females.
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The concept of PEComa has gained wide acceptance and these lesions have been described in numerous anatomic sites since the term was coined by Bonetti et al (1) in 1992.
The company also sold to LaBouchere, a Dutch bank; Modderkolk, an electrical engineering firm, and Pecoma, a Magic VAR who developed a subscriber management system for publisher Wolters Kluwer.
Similarly to gp100, angiomyolipoma, sugar cell tumor of lung, lymphangioleiomyomatosis, and pecoma also express MART1.
We report the occurrence of an adrenal PEComa arising in a 50-year-old man.
Early on, our group proposed LAM as a member of the "perivascular epithelioid cell tumors," (17-19) a wide family of proliferative lesions that we named PEComas and that has been widely recognized and incorporated in the World Health Organization nomenclature (PEComa: "a mesenchymal tumor composed of histologically and immunohistochemically distinctive perivascular epithelioid cells" [PECs]).
The PEComa family of tumors includes angiomyolipoma, lymphangioleiomyomatosis, clear cell sugar tumor of the lung, and clear cell myomelanocytic tumor of the falciform ligament/ligamentum teres.
In 1996, Zamboni et al (4) reported the first case of pancreatic CCST and suggested the name PEComa for these neoplasms composed of a pure proliferation of PECs.
Tumors that may be confused with PENs include solid serous adenoma, (61,62) PEComa (clear cell "sugar" tumor), (63) and paraganglioma.
The PEComa concept is still controversial and not universally accepted, as perivascular epithelioid cells are not detected in normal tissues.
Archimedes simplifies software installation so that KPN's employees will have access to up-to-date, robust applications more quickly than they do now," said Jan Veldsink, business consultant for Pecoma Informatica, the Netherlands-based IT company that developed Archimedes.
1-4) Angiomyolipoma, including its epithelioid variant, belongs to the family of tumors with perivascular epithelioid differentiation, that is, PEComas, which include clear cell myomelanotic tumor of the falciform ligament, ligamentum teres, and common bile duct; lymphangio(leio)myomatosis; pulmonary and extrapulmonary clear cell "sugar" tumors; and a group of rare, morphologically and immunohistochemically similar lesions seen at other sites.