PEComa

PEComa

A group of mesenchymal tumors composed of epithelioid and spindle cells displaying perivascular epithelioid (PEC) differentiation. The PEComa family of tumors includes angiomyolipoma, clear-cell "sugar" tumor of lung and gastrointestinal tract and other sites, lymphangioleimyomatosis, clear-cell myomelanocytic tumor of the falciform ligament.

PEComa

A rare, possibly mesenchymal tumour of unknown origin and of uncertain malignant potential, which can arise anywhere in the body and more commonly affects females.
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In 1996, Bonnetti's colleague, Zamboni, delineated perivascular epithelioid cells in both angiomyolipoma (AML) and clear cell "sugar" tumor of the lung and coined the term PEComa [2].
This case report aimed to present a patient who undergone retroperitoneoscopic partial nephrectomy due to a renal mass and diagnosed with PEComa after pathological examination.
Angiomyolipoma (AML) has undergone a remarkable transformation in recent years, from a rare and rather pedestrian tumor type restricted to kidney, to a biologically fascinating and morphologically heterogenous entity which can occur in a wide variety of sites and which has been given the collective name of PEComa (5).
ABI-009 is currently being evaluated in a clinical trial for the treatment of patients with advanced perivascular epithelioid cell tumors (PEComa), an extremely rare form of sarcoma.
Renal angiomyolipomas (AMLs) are the most common benign renal tumors, now considered among the family of perivascular epithelioid cell tumors (PEComa) and divided into two histological categories: triphasic AMLs and monotypic epithelioid AMLs [15].
Angiomyolipomas (AMLs) are the most common mesenchymal renal neoplasms and are classified as neoplasms of perivascular epithelioid cells (PEComa).
Primary PEComa of the bladder treated with primary excision and adjuvant interferon-alpha immunotherapy: a case report.
Angiomyolipomas (AMLs), a type of perivascular epithelioid cell tumor (PEComa), are the most common benign tumor of the kidney, yet are relatively uncommon in the general population, occurring in 0.3%-2.1% of people.
El objetivo del trabajo fue describir por primera vez las caracteristicas de un tumor espontaneo de ovario con morfologia similar a la de los tumores de celulas epitelioides perivasculares (PEComa) en un ejemplar adulto de boga (Leporinus obtusidens) obtenido del rio Parana (Argentina).
(3) In recent years there have also been at least 8 reported cases of perivascular epithelioid cell tumour (PEComa) of the bladder.
In this case, a broad differential diagnosis of carcinoma, endometrial stromal tumour and PEComa were made histopathologically.