Summary: Retroperitoneal fibrosis is the rare disease also known as Ormond's disease
. Retroperitoneal fibrosis is characterized by the inflammatory disorder in which abnormal formation of tissue or fibrosis occurs in the back of the abdominal cavity and behind the retro membrane.
The DDx includes idiopathic retroperitoneal fibrosis (Ormond's disease
Rethinking Ormond's disease
: "idiopathic" retroperitoneal fibrosis in the era of IgG4-related disease.
A variety of terms have been used to describe the disorder, including Ormond's disease
, periureteritis fibrosa, periureteritis plastica, chronic periureteritis, sclerosing retroperitoneal granuloma, and fibrous retroperitonitis.
Herein, we present a case of tumour associated embolism in a patient with suspected Ormond's disease.
A computed tomography (CT) scan on the other hand showed diffuse proliferation of fibrous tissue in the retroperitoneum, compatible with Ormond's disease (Figure 1).