They are frequently seen in the organ of Zuckerkandl
, near the inferior mesenteric artery origin.
They are most frequently found in the organ of Zuckerkandl
(around the root of the inferior mesenteric artery), but it also may be uncovered in other locations, such as retroperitoneum and the urinary bladder.
The mass was identified at the aortic bifurcation at the organ of Zuckerkandl
and was successfully excised, including resection of a portion of the aortic wall.
They can present anywhere along the sympathetic paraganglia chains from the neck to the pelvis, but they occur most often intra-abdominally in the periaortic region and the organ of Zuckerkandl
8,9) Normal paraganglionic tissue has also been described at the root of the inferior mesenteric artery, which serves as the superior limit of the organ of Zuckerkandl
Extra-adrenal paragangliomas are usually intra-abdominal and arise around the renal hilum, the adrenal gland or organ of Zuckerkandl
, but approximately 10% of these tumours occur in the urinary bladder and account for less than 0.
To the Editor: Few cases of tumors of the organ of Zuckerkandl with electrocardiogram (ECG) patterns suggestive of acute myocardial infarction related to the effect of excess circulating catecholamines are described in the literature.
The area known as the organ of Zuckerkandl encompasses all extra-adrenal chromaffin tissue near the origin of the inferior mesenteric artery and the aortic bifurcation.
We presented a case of extra-adrenal norepinephrine-secreting paraganglioma of the organ of Zuckerkandl in a patient who had surgical removal of the tumor with subsequent development of symptoms and ECG changes mimicking those of myocardial infarction.
The area known as the organ of Zuckerkandl (aorticosympathetic group) encompasses all extra-adrenal chromaffin tissue near the origin of the inferior mesenteric artery and the aortic bifurcation.
The behavior of paragangliomas of the organ of Zuckerkandl is known to be more malignant than in those found elsewhere.
The symptoms of tumor arising in the organ of Zuckerkandl may be those related either to the growth of a retroperitoneal mass or to excessive catecholamine secretion.