hemifacial microsomia

(redirected from Oral-mandibular-auricular syndrome)

hemifacial microsomia



A rare congenital anomaly, usually inherited sporadically, in which one side of the body, usually the right, fails to develop equally with the left. The ear, nose, and maxilla on the affected side are hypoplastic. In addition the right lung and kidney may be smaller than normal, and affected children often have ventriculoseptal defects. Surgical treatment of facial defects associated with HFM is often undertaken by combined teams of oral and maxillofacial surgeons. Synonym: facio-auriculo vertebral syndrome; Goldenhar syndrome; oculoauricular vertebral dysplasia

hemifacial microsomia (HFM) (hem´ifā´shəl mī´krəsō´mēə),

n a condition in which one side of the lower face fails to develop properly. It is characterized by the malformation of the ear on the affected side and defects in the structure of the mandible. It is the second most common birth defect after clefts. Also called
brachial arch syndrome, oral-mandibular-auricular syndrome, lateral facial dysplasia, or otomandibular dysostosis.