nephrogenic systemic fibrosis

(redirected from Nephrogenic fibrosing dermopathy)
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nephrogenic systemic fibrosis

A rare condition linked to gadolinium-based MRI contrast solutions—in particular Omniscan and OptiMARK, which have a linear non-ionic structure and more likely to release Gd3+ to tissue—characterised by fibrosis of skin, joints, eyes and internal organs, resulting in scleromyxedema/papular mucinosis-like histologic appearance, limitation of joint movement, kidney failure and, in extreme cases, systemic fibrosis affecting the lungs, heart and liver.
 
Prevention
Some protection may be provided by diethylene-triaminepentaacetic acid.
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Gadolinium--a specific trigger for the development of nephrogenic fibrosing dermopathy and nephrogenic systemic fibrosis?
Gadolinium deposition in nephrogenic fibrosing dermopathy.
Nephrogenic fibrosing dermopathy (scleromyxedema-like illness of renal disease).
Gadolinium: a specific trigger for the development of nephrogenic fibrosing dermopathy and nephrogenic systemic fibrosis?
The Web site address is the acronym for the International Center for Nephrogenic Fibrosing Dermopathy Research.
Gadolinium-A specific trigger for the development of nephrogenic fibrosing dermopathy and nephrogenic systemic fibrosis?
Nephrogenic fibrosing dermopathy after liver transplantation successfully treated with plasmapheresis.
Calciphylaxis and metastatic calcification associated with nephrogenic fibrosing dermopathy.
Currently, 175 cases have been reported to the International Center for Nephrogenic Fibrosing Dermopathy Research.
Nephrogenic systemic fibrosis: the nosological and conceptual evolution of nephrogenic fibrosing dermopathy.
When nephrogenic fibrosing dermopathy was originally identified in 8 of 265 kidney transplant recipients at a single Southern California transplant center, it seemed likely to be due to some infectious entity at that site.
A very small case-control study among the original cluster of patients showed that those with nephrogenic fibrosing dermopathy were more likely than others to have had less than optimal renal function after transplantation, requiring hemodialysis and medications associated with severe disease.