Non-ketotic hyperglycaemic hemichorea-hemiballismus (NKHHC) is a rare, reversible condition, with the clinical and radiological signs usually resolving within 6 months, following correction of hyperglycaemia.
We describe a paediatric patient presenting with the classic clinical and radiological findings of NKHHC.
The diagnosis of NKHHC is that of a classic triad of clinical presentation (hemichorea-hemiballismus), radiological features and clinical resolution of symptoms with glycaemic control.
The clinical characteristics of the movements in NKHHC are that they are unilateral and involuntary, follow a poorly defined pattern and develop over a period of hours.
The pathophysiology of NKHHC is poorly understood, and there are two current theories.
The treatment of NKHHC is aggressive glycaemic control.