Mounier-Kuhn syndrome (MKS) is an infrequent congenital syndrome, whose hallmark is airway enlargement.
Lorenzin et al., "Renal transplantation in a patient affected by Mounier-Kuhn syndrome," Transplantation Proceedings, vol.
Gangadharan et al., "Airway stenting and tracheobronchoplasty improve respiratory symptoms in Mounier-Kuhn syndrome," Chest, vol.
Mounier-Kuhn syndrome is a rare congenital anomaly characterized by the presence of dilated trachea and major bronchi.
A possibility of Mounier-Kuhn syndrome was considered and patient was subjected to bronchoscopy.
Mounier-Kuhn syndrome (MKS) also known as tracheobronchomegaly is an uncommon condition characterized by dilatation of the trachea and major bronchi.
, a rare, most likely congenital, disorder can be mistaken for tracheal diverticulum because it involves dilatation of the trachea and main stem bronchi, with folds of redundant mucosa and fibromuscular tissue that resemble diverticula.
On further evaluation computed tomography scan of the chest (plain) revealed dilated trachea and mainstem bronchi with multiple sacculations in the proximal part of thoracic part of trachea involving posterolateral walls with tractional and tubular bronchiectasis in bilateral lung fields which confirms it as a case of Mounier-Kuhn syndrome which is a rare cause of bronchiectasis and should be considered in differentials of lower respiratory tract infections.
Mounier-Kuhn syndrome: a rare cause of severe bronchial dilatation with normal pulmonary function test: a case report.