Mounier-Kuhn syndrome (MKS) is an infrequent congenital syndrome, whose hallmark is airway enlargement.
Lorenzin et al., "Renal transplantation in a patient affected by Mounier-Kuhn syndrome," Transplantation Proceedings, vol.
Mounier-Kuhn syndrome is a rare congenital anomaly characterized by the presence of dilated trachea and major bronchi.
A possibility of Mounier-Kuhn syndrome was considered and patient was subjected to bronchoscopy.
On further evaluation computed tomography scan of the chest (plain) revealed dilated trachea and mainstem bronchi with multiple sacculations in the proximal part of thoracic part of trachea involving posterolateral walls with tractional and tubular bronchiectasis in bilateral lung fields which confirms it as a case of Mounier-Kuhn syndrome which is a rare cause of bronchiectasis and should be considered in differentials of lower respiratory tract infections.
Mounier-Kuhn syndrome: a rare cause of severe bronchial dilatation with normal pulmonary function test: a case report.
Tels sont les propos de Rached Ghannouchi a la journaliste Angelique Mounier-Kuhn
du journal suisse [beaucoup moins que] Le Temps [beaucoup plus grand que] (edition du mardi 14 janvier 2014 ) .
syndrome, a rare, most likely congenital, disorder can be mistaken for tracheal diverticulum because it involves dilatation of the trachea and main stem bronchi, with folds of redundant mucosa and fibromuscular tissue that resemble diverticula.