Mondini dysplasia


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Mon·di·ni dys·pla·si·a

(mōn-dē'nē),
congenital anomaly of osseus and membranous otic labyrinth characterized by aplastic cochlea and deformity of the vestibule and semicircular canals with partial or complete loss of auditory and vestibular function; may be associated with dilated vestibular aqueduct and spontaneous cerebrospinal fluid otorrhea resulting in meningitis.
See also: Mondini hearing impairment.
Farlex Partner Medical Dictionary © Farlex 2012

Mon·di·ni dys·pla·sia

(mon-dē'nē' dis-plā'zē-ă)
Congenital anomaly of osseus and membranous labyrinth characterized by aplastic cochlea, and deformity of the vestibule and semicircular canals with partial or complete loss of auditory and vestibular function; may be associated with spontaneous cerebrospinal fluid otorrhoea resulting in meningitis.
Medical Dictionary for the Health Professions and Nursing © Farlex 2012
References in periodicals archive ?
proposed a new classification system for congenital inner ear malformations based on CT imaging, which divided inner ear malformations up into those of labyrinthine aplasia (Michel deformity), cochlear aplasia, cochlear hypoplasia, incomplete partition (Mondini dysplasia) and common cavity defects.1 The pathogeneses of the various defects were explained by arrested development of the inner ear at different stages.
reported on 2 children and their mother, all of whom had Mondini dysplasia. (6) The children were 5 and 9 years old, and demonstrated abnormal findings on vestibular testing but were otherwise asymptomatic for vestibular function impairment.
Recurrent meningitis and Mondini dysplasia. Arch Otolaryngol Head Neck Surg.
"The use of cochlear implantation to treat patients with inner ear malformations such as Mondini dysplasia has been increasingly successful the world over," he said.
Spontaneous cerebrospinal fluid otorrhea in association with a congenital defect of the cochlear aqueduct and Mondini dysplasia. Neurosurgery 1982;11:356-62.