LDHA, lactate dehydrogenase A; LDHB, lactate dehydrogenase B; PDHA1, pyruvate dehydrogenase (lipoamide) alpha 1; DLAT, dihydrolipoamide S-cetyltransferase; DLD, dihydrolipoamide dehydrogenase; GK, glycerol kinase; GPD1, glycerol-3-phosphate dehydrogenase 1; GPD2, glycerol -3-phosphate dehydrogenase 2; ACSS3, acyl CoA synthetase short chain family member 3; PCCA, propionyl CoA carboxylase alpha; PCCB, propionyl CoA carboxylase beta; MCEE,
methylmalonyl CoA epimerase; MUT,
methylmalonyl CoA mutase.
Methionine synthase (in the cytosol) requires methylcobalamin as cofactor, and
methylmalonyl CoA mutase (in mitochondria) requires 5' deoxyadenosylcobalamin as coenzyme.