MPS IH | definition of MPS IH by Medical dictionary
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References in periodicals archive
Hurler's syndrome (MPS IH
), which is a prototype of MPS is caused by a deficiency of alpha-L-iduronidase due to a loss of function mutation leading to excessive accumulation of partially degraded GAGs, dermatan sulphate and heparan sulphate within the cells.
Medial hemiepiphysiodesis has been shown to be quite successful in children with Hurler syndrome (MPS IH
) after hematopoietic stem cell transplant.^ The implants shown here utilize a tension band plate and screws and represent a fairly new device in the care of angular deformities in children.