hypoplastic left heart syndrome

(redirected from Left heart hypoplasia)

hypoplastic left heart syndrome

congenital hypoplasia or atresia of the left ventricle, the aortic or mitral valve, and the ascending aorta, with respiratory distress, cardiac failure, and death in infancy.

hy·po·plas·tic left heart syn·drome

association of underdevelopment of the left heart chambers with atresia or stenosis of the aortic and/or mitral valve and hypoplasia of the ascending aorta.

hypoplastic left heart syndrome (HLHS)

any of a group of congenital anomalies consisting of hypoplasia or atresia of the left ventricle and of the aortic or mitral valve or both and hypoplasia of the ascending aorta. It is characterized by respiratory distress and extreme cyanosis, with cardiac failure and death in early infancy.

hypoplastic left heart syndrome

Pediatric cardiology A group of congenital often AR cardiac defects characterized by hypo- or agenesis of the left ventricle, aortic and mitral valves, an atrial right-to-left shunt; right-sided hypoplasia of tricuspid or pulmonary valves, pulmonary stenosis, or right ventricular hypoplasia; the ascending and transverse aorta is narrowed with a diaphragm-like aortic coarctation at the preductal aortic isthmus; postnatal life hinges on adequate blood supply–ie, is ductus dependent, unrestricted atrial shunting, and a balance between the pulmonary and systemic vascular resistances; surgery is difficult as there are extensive malformations Mortality High. See Baby Fae heart.


characterized by hypoplasia, e.g. hypoplastic anemia.

hypoplastic left heart syndrome
a congenital anomaly seen in cats in which there is mitral atresia and incomplete development of the left ventricle and aortic valve.