Kartagener syndrome

Kar·ta·ge·ner syn·drome

(kahr-tag'ĕ-nĕr), [MIM*244400]
complete situs inversus associated with bronchiectasis and chronic sinusitis associated with ciliary dysmotility and impaired ciliary mucous transport in the respiratory epithelium. The mechanism of the reversal of laterality remains an enigma, but it appears to be strictly an abolition (indifference) of laterality rather than a true reversal. Autosomal recessive inheritance with variable penetrance.
See also: immotile cilia syndrome.

Kartagener syndrome

Immotile cilia syndrome A trio of sinusitis, bronchitis and situs inversus–lateral reversal of all organs in the chest and abdomen–ie, heart and stomach on right, liver on left, etc–ie, opposite or inverted from their usual position

Kar·ta·ge·ner syn·drome

(kahr-tag'ĕ-nĕr sin'drōm)
Complete situs inversus associated with bronchiectasis and chronic sinusitis associated with ciliary dysmotility and impaired ciliary mucus transport in the respiratory epithelium; autosomal recessive inheritance with variable penetrance. The mechanism of the reversal of laterality remains an enigma, but it appears to be strictly an abolition (indifference) of laterality rather than a true reversal.

Kartagener,

Manes, Swiss physician, 1897-1975.
Kartagener syndrome - complete situs inversus associated with bronchiectasis and chronic sinusitis. Synonym(s): Kartagener triad; Zivert syndrome
Kartagener triad - Synonym(s): Kartagener syndrome

Kar·ta·ge·ner syn·drome

(kahr-tag'ĕ-nĕr sin'drōm) [MIM*244400]
Complete situs inversus associated with bronchiectasis and chronic sinusitis associated with ciliary dysmotility and impaired ciliary mucous transport in the respiratory epithelium.
References in periodicals archive ?
She is also among the 50% of people who have PCD to also have Kartagener syndrome, which means her organs are in mirror image, with her heart and stomach on the right-hand side and her lungs are not identical to each other.
Birth of a healthy boy using fresh testicular sperm in a patient with Klinefelter syndrome combined with Kartagener syndrome.
A heart-lung transplantation has been performed in two patient suffering from the complete Kartagener Syndrome.
Conversley, 50% of those with primary ciliary dyskinesia have DSIT, a condition called Kartagener syndrome (triad of bronchiectasis, chronic sinusitis, and situs inversus).
Kartagener syndrome (KS), a subset of primary ciliary dyskinesia, is an autosomal recessive disorder with variable phenotypic expressions.
Kartagener syndrome is an autosomal recessive disorder, a subgroup of primary ciliary dyskinesia, characterized by a triad of bronchiectasis, sinusitis and situs inversus.
If associated with primary ciliary dyskinesia, sinusitis and bronchiectasis and infertility in males, it is called Kartagener Syndrome found in 25% of patients (3).
They present as Kartagener syndrome [1] with the classic triad of situs inversus, chronic sinusitis and bronchiectasis.
The patient was diagnosed as Kartagener syndrome with classical triad of bronchiectasis, sinusitis, situs inversus and with mucociliary dysfunction.
Named Kartagener syndrome after the doctor, the disorder affects about 1 in every 10,000 people.
Consideration should be given to this imaging technique early in the presentation of Kartagener syndrome, when a chest radiograph may not be sensitive enough to identify disease processes or when another differential is being considered.
3,4) Kartagener syndrome is included as a subgroup or part of the primary ciliary dyskinesia.