It occurs more commonly in the autosomal dominant form (Romano-Ward syndrome) and rarely as the autosomal recessive Jervell
and Lange-Nielsen syndrome (associated with sensorineural hearing loss).
[6.] Lie H, Karl MR, Kurwijila LR and AM Jervell
Improving smallholder livelihoods through local value chain development: A case study of goat milk yogurt in Tanzania.
Syndromes associated with hearing loss or progressive or late- onset hearing loss such as neurofibromatosis, osteopetrosis and Usher syndrome; other frequently identified syndromes include Waardenburg, Alport, Pendred and Jervell
[30.] Abdul-Rahim HF, Husseini A, Bjertness E, Giacaman R, Gordon NH, Jervell
Out of these KCNQ1 which is a potassium channel gene, its heterozygous mutation causes RWS while its homozygous mutation causes a much rarer condition Jervell
Lange-Nielsen syndrome in which along with long QT interval deafness also occurs.1-9
Abdul-Rahim H, Husseini A, Bjertness E, Giacaman R, Gordon N, Jervell
(11) Anne Moxnes Jervell
, 'Changing Patterns of Family Farming and Pluriactivity' (1999) 39(1) Sociologia Rural is 100.
Hypothetically, it can be seen that entrepreneur business growth stems from effective resource management through conventional management practice and fortunate access to resources (Jervell
, 2011; Bruck et al, 2011; Bennet, 2010; Parker, 2008).
Renting, H., van Oostindie, H., Laurent, C., Brunori, G., Brajolle, D., Jervell
, A.M., Granberg, L., Heinonen, M.
Consideration can also be given to obtaining an EKG on all children with sensorineural hearing loss, given the morbidity and mortality associated with the prolonged QT interval in Jervell
and Lange-Nielsen syndrome.
Mink gene mutations can lead to various malignant arrhythmias such as familial long QT syndrome ([LQT.sub.S]) and Jervell
syndrome [24, 25].
Objective: To identif y the patients of Jervell
and Lange-Nielsen syndrome (JLNS) amongst congenitally deaf children.