After cessation of bile flow, dilatation of extrahepatic and
intrahepatic bile ducts and alteration of portal tracts occur in a few days.
In ERCP, dilatation of common bile duct with multiple filling defects was seen, but gallbladder and
intrahepatic bile ducts were normal (Figure 2).
Loss of
intrahepatic bile ducts or ductopenia is usually designated when bile ducts are absent in at least 50% of portal tracts provided that at least 10 portal tracts are available for assessment.
4) Autoimmune-mediated destruction of
intrahepatic bile ducts eventually leads to bile flow obstruction, hepatic fibrosis, cirrhosis, and eventual liver failure.
Intrahepatic bile duct adenomas are rare, benign tumors composed of disorganized but mature peribiliary gland acini and tubules.
5] Caroli's disease is characterized by segmental dilatation of the
intrahepatic bile ducts without hepatic fibrosis as compared to Caroli's syndrome, which is defined as ectasia of the
intrahepatic bile ducts with hepatic fibrosis.
If US demonstrates dilated
intrahepatic bile ducts and a hilar tumour is suspected, MRCP is the next investigation of choice, as more accurate non-invasive imaging of the level and extent of the bile duct obstruction is obtained (Fig.
Cholangiocarcinomas arise from the biliary ductal epithelium, most commonly in the bifurcation of the
intrahepatic bile ducts.
The
intrahepatic bile ducts, CHD, CBD and intrahepatic veins were unremarkable.
Biliary atresia is an inflammatory cholangiopathy of infancy that results in progressive fibrosis and obliteration of extrahepatic and
intrahepatic bile ducts.
INTRODUCTION: Jacques Carole in 1958 first described a rare disease with multifocal, segmental, saccular dilatation of the large
intrahepatic bile ducts, which causes stagnation of bile formation of biliary sludge and stones.
This protocol applies to carcinomas of the
intrahepatic bile ducts and mixed hepatocellular-cholangiocarcinoma.
