hemifacial microsomia


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hemifacial microsomia

(mi?kro-so'me-a),

HFM

A rare congenital anomaly, usually inherited sporadically, in which one side of the body, usually the right, fails to develop equally with the left. The ear, nose, and maxilla on the affected side are hypoplastic. In addition the right lung and kidney may be smaller than normal, and affected children often have ventriculoseptal defects. Surgical treatment of facial defects associated with HFM is often undertaken by combined teams of oral and maxillofacial surgeons. Synonym: facio-auriculo vertebral syndrome; Goldenhar syndrome; oculoauricular vertebral dysplasia

hemifacial microsomia (HFM) (hem´ifā´shəl mī´krəsō´mēə),

n a condition in which one side of the lower face fails to develop properly. It is characterized by the malformation of the ear on the affected side and defects in the structure of the mandible. It is the second most common birth defect after clefts. Also called
brachial arch syndrome, oral-mandibular-auricular syndrome, lateral facial dysplasia, or otomandibular dysostosis.
References in periodicals archive ?
Nonsurgical Treatment of Hemifacial Microsomia by Therapeutic Ultrasound and Hybrid Functional Appliance- Journal of Clinical Trials 2010: 2 29-36.
Hemifacial microsomia has a wide phenotypic variation and no uniform criterion for diagnosis exists.
Bone distraction in patient with Grade II hemifacial microsomia
The propellant unilateral magnetic appliance (PUMA) a new technique for hemifacial microsomia.
In 1993, Inigo et al reported on the treatment of patients with hemifacial microsomia with a cross-facial technique in which the sural nerve was anastomosed to the donor side and tunneled supralabially; then its fascicles were sutured directly to perioral muscles.
The orthognathic surgery assisted by Narticulator will prepare CT scan beforehand to simultaneously conduct 3D symmetry analysis and 3D bony cephalometry during planning, said Fang, and the procedure enhancing the accuracy has been applied to correct cases like temporomandibular joint abnormalities (of TMJ), hemifacial microsomia, facial asymmetry, and complex facial disharmonies.
The associated anomalies included preauricular skin tags, sinus in the cheek, vascular malformation, well developed but small accessory ears, microtia and hemifacial microsomia.
In the long standing cases, facial asymmetry is similar to mild hemifacial microsomia in unilateral cases and retrognathia, micrognathia or microgenia in bilateral cases, presenting with a bird face like appearance.
Inclusion criteria: Patients with mandibular hypo plasia and with hemifacial microsomia as well as patients with facial asymmetry with deviation of chin to the affected side.
com 2,3,4,7,9 HEMANGIOMA See Craniofacial Disorders HEMIDYSPLASIA, UNILATERAL See: Ichthyosis HEMIFACIAL MICROSOMIA See: Goldenhar Syndrome HEMIHYPERTROPHY See: Beckwith-Wiedeman Syndrome HEMIMEGALENCEPHALY Hemimegalencephaly Support Group Sue Cowper 40 Olympic Ave.
com/~kdswhrt/ 2,3,4,7,9 HEMANGIOMA See: Craniofacial Disorders HEMIDYSPLASIA, UNILATERAL See: Ichthyosis HEMIFACIAL MICROSOMIA See: Goldenhar Syndrome HEMIHYPERTROPHY See: Beckwith-Wiedeman Syndrome HEMIPLEGIA, ALTERNATING See also: Epilepsy; Seizure Disorders International Foundation for Alternating Hemiplegia of Childhood 239 Nevada St.