hypoplastic left heart syndrome(redirected from HLHS)
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hypoplastic left heart syndrome
congenital hypoplasia or atresia of the left ventricle, the aortic or mitral valve, and the ascending aorta, with respiratory distress, cardiac failure, and death in infancy.
Miller-Keane Encyclopedia and Dictionary of Medicine, Nursing, and Allied Health, Seventh Edition. © 2003 by Saunders, an imprint of Elsevier, Inc. All rights reserved.
hy·po·plas·tic left heart syn·drome[MIM*241550]
association of underdevelopment of the left heart chambers with atresia or stenosis of the aortic and/or mitral valve and hypoplasia of the ascending aorta.
Farlex Partner Medical Dictionary © Farlex 2012
hypoplastic left heart syndromePediatric cardiology A group of congenital often AR cardiac defects characterized by hypo- or agenesis of the left ventricle, aortic and mitral valves, an atrial right-to-left shunt; right-sided hypoplasia of tricuspid or pulmonary valves, pulmonary stenosis, or right ventricular hypoplasia; the ascending and transverse aorta is narrowed with a diaphragm-like aortic coarctation at the preductal aortic isthmus; postnatal life hinges on adequate blood supply–ie, is ductus dependent, unrestricted atrial shunting, and a balance between the pulmonary and systemic vascular resistances; surgery is difficult as there are extensive malformations Mortality High. See Baby Fae heart.
McGraw-Hill Concise Dictionary of Modern Medicine. © 2002 by The McGraw-Hill Companies, Inc.