hypoplastic left heart syndrome

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hypoplastic left heart syndrome

 
congenital hypoplasia or atresia of the left ventricle, the aortic or mitral valve, and the ascending aorta, with respiratory distress, cardiac failure, and death in infancy.

hy·po·plas·tic left heart syn·drome

[MIM*241550]
association of underdevelopment of the left heart chambers with atresia or stenosis of the aortic and/or mitral valve and hypoplasia of the ascending aorta.

hypoplastic left heart syndrome

Pediatric cardiology A group of congenital often AR cardiac defects characterized by hypo- or agenesis of the left ventricle, aortic and mitral valves, an atrial right-to-left shunt; right-sided hypoplasia of tricuspid or pulmonary valves, pulmonary stenosis, or right ventricular hypoplasia; the ascending and transverse aorta is narrowed with a diaphragm-like aortic coarctation at the preductal aortic isthmus; postnatal life hinges on adequate blood supply–ie, is ductus dependent, unrestricted atrial shunting, and a balance between the pulmonary and systemic vascular resistances; surgery is difficult as there are extensive malformations Mortality High. See Baby Fae heart.
References in periodicals archive ?
Within this growing collaboration, seven hospitals and an advocacy group work together to provide care for HLHS patients across the U.S.
In HLHS, the left ventricle is significantly underdeveloped, and the heart can't pump sufficient blood through the body.
HLHS is a rare combination of cardiac defects where the left side of the heart and surrounding structures are so severely underdeveloped that they are unable to function.
Her final achievement in which she was HLHS study had done which celebrated of the success for votes for Hilary has unsung heroes makes the in our own vibrant.
These defects are rare and include diagnoses such as transposition of the great arteries, HLHS with a restrictive or closed foramen ovale, and CHD with associated heart failure and hydrops.
The complexity of the HLHS anomaly warrants several procedures within the first two years of life, leading to prolonged hospitalizations.
Fatal heart diseases such as HLHS demand the best quality of medical imaging for the planning of paediatric open-heart surgery, added Dr Alsheikh Ali, who is the chair of the Cardiac Sciences Institute at the hospital.
The patient was born with hypoplastic left heart syndrome (HLHS), where the left ventricle of the heart was very underdeveloped and unable to pump blood to the body.
Higher incidence of VSD and TA was found as compared to other series, and relatively lower incidence of HLHS. On analyzing the post natal scans 3 with detected small VSDs were normal.
The trial aims to determine how stem cells from autologous umbilical cord blood can help children with hypoplastic left heart syndrome (HLHS), a rare defect in which the left side of the heart is critically underdeveloped.