Gierke disease
gly·co·ge·no·sis type 1
(glī'kō-jĕ-nō'sis tīp)Disorder due to glucose-6-phosphatase deficiency, resulting in accumulation of excessive glycogen of normal chemical structure, particularly in liver and kidney.
Synonym(s): Gierke disease, von Gierke disease.
Synonym(s): Gierke disease, von Gierke disease.
Medical Dictionary for the Health Professions and Nursing © Farlex 2012
Gierke disease
(ger'ke) [Edgar von Gierke, Ger. pathologist, 1877–1945]
Glycogen storage disease type 1a.Medical Dictionary, © 2009 Farlex and Partners
Gierke,
Edgar von, German pathologist, 1877-1945.Fibiger-Debré-von Gierke syndrome - Synonym(s): Debré-Fibiger syndrome
Gierke disease - glycogenosis due to glucose 6-phosphatase deficiency, resulting in accumulation of excessive amounts of glycogen of normal chemical structure, particularly in liver and kidney. Synonym(s): type 1 glycogenosis; von Gierke disease; von Gierke syndrome
von Gierke disease - Synonym(s): Gierke disease
von Gierke syndrome - Synonym(s): Gierke disease
Medical Eponyms © Farlex 2012