Gargoyle Cell

A cell, usually a histiocyte, engorged with mucopolysaccharide-laden dermatan sulfate and heparan sulfate lysosomes, seen in patients with Hurler syndrome or mucopolysaccharidosis type I-H, due to alpha-l-iduronidase deficiency
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References in periodicals archive ?
[2] The PVS dilatation reflects impairment of CSF re-absorption owing to accumulation of GAGs in the vacuolated gargoyle cells [3] of the leptomeninges.