From July 2006 to April 2016, TVP or TVR was performed in 245 Ebstein's anomaly
Surgical management of Ebstein's anomaly
in the adult.
The following are the hemodynamic goals for the management of TOF and Ebstein's anomaly
: avoid a drop in systemic vascular resistance; maintain intravascular volume and venous return; prevent hypoxemia, hypercapnea and acidosis, as well as myocardial depression during anesthesia (12).
The spectrum of Ebstein's anomaly
of the tricuspid valve.
Echocardiogram also showed severe right heart enlargement with atrialization of the right ventricle and apical displacement of the tricuspid valve consistent with Ebstein's anomaly
, which can be seen in Figures 1 and 4.
Suarez et al reported a case of graded epidural anaesthesia being used for caesarean section in a patient with Ebstein's anomaly
in whom hypotension was managed successfully with crystalloids and phenylephrine.
Mothers with cyanotic congenital heart disease have higher incidence of fetal losses, preterm births and low weight neonates; however in Ebstein's anomaly
it is considered that even without cyanosis, fetal morbidity is high with an increased incidence of congenital problems (8).
Chest X-ray showed enlarged right atrium with cardiomegaly, while 2D echocardiogram showed the presence of moderately enlarged right atrium and ventricle, tricuspid regurgitation with downwardly displaced tricuspid valves, confirming diagnosis of Ebstein's anomaly
. There was no atrial septal defect or pulmonary hypertension.
Morphologic spectrum of Ebstein's anomaly
of the heart: a review.
Many of us learned in medical school that lithium is a known teratogen and should not be used in pregnancy, but we now know that its teratogenicity is relatively modest: The risk of Ebstein's anomaly
is about 0.05% among babies exposed to lithium in the first trimester.
Sue suffered from Ebstein's Anomaly
, a rare congenital heart condition.
 There is an association between MVP and other congenital heart diseases such as ostium secundum atrial septal defect, hypertrophic cardiomyopathy, Marfan's syndrome, Ebstein's anomaly
and Wolf Parkinson White (WPW) syndrome, although these are rare occurrences.