Long-term outcome of congenital cystic adenomatoid malformation
. Pediatr Surg Int 1999;15:332-5.
Primary pulmonary rhabdomyosarcoma arising within cystic adenomatoid malformation
: a case report and review of the literature.
Congenital cystic adenomatoid malformations
(CCAMs) are congenital lung malformations derived from a hamartomatous lesion of the bronchial tree (1).
In the first thorax CT taken, an appearance in line with cystic adenomatoid malformation
and consolidation was present in left lung upper lobe (Figure 2).
Baldi, "Cystic adenomatoid malformation
of the lung in an adult," Minerva Chirurgica, vol.
Congenital cystic diseases of the lung and mediastinum include congenital cystic adenomatoid malformation
(CCAM), bronchopulmonary "sequestration", congenital lobar emphysema, broncogenic cyst, esophageal duplication cysts and neurogenic cysts (1).
In the fetus, polidocanol has been used for fetal intralobar bronchopulmonary sequestration and for congenital cystic adenomatoid malformation
of the lung.
Of four cases with cardiac malposition caused by extracardiac congenital malformation,two cases had mesoposition dueto pleural effusion, one case had dextroposition due to left-sided congenital diaphragmatic hernia, and one case had an extreme levoposition due to cystic adenomatoid malformation
in the right lung (Table 1).
Congenital cystic adenomatoid malformation
(CCAM) of the lungs is a developmental abnormality (hamartoma) (1).
Histopathological examination showed congenital cystic adenomatoid malformation
(112,113) Mucinous cells in pulmonary congenital cystic adenomatoid malformation
share the same differentiation profile (including the expression of MUC5AC) and molecular abnormalities (frequent K-ras mutation) as mBAC and can then be considered as a precursor lesion of this entity.