coproporphyrinogen oxidase


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cop·ro·por·phy·rin·o·gen ox·i·dase

an enzyme that catalyzes a step in porphyrin biosynthesis, reacting coproporphyrinogen III and O2 to form protoporphyrinogen IX and 2CO2. A deficiency of this enzyme will result in hereditary coproporphyria.
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The association between genetic polymorphisms of coproporphyrinogen oxidase and an atypical porphyrinogenic response to mercury exposure in humans.
Urinary porphyrin excretion in neurotypical and autistic children
In patient B, erythrocyte PBGD, uroporphyrinogen-III synthase, and uroporphyrinogen decarboxylase as well as lymphocyte coproporphyrinogen oxidase, protoporphyrinogen oxidase, and ferrochelatase activities were additionally examined; all were within reference values.
The excessive urinary coproporphyrin excretion cannot be caused by an enzymatic deficiency, because coproporphyrinogen oxidase activity was within reference values.
5-aminolevulinic acid dehydratase deficiency porphyria: a twenty-year clinical and biochemical follow-up

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