Arnold-Chiari malformation

(redirected from Chiari malformation)
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Ar·nold-Chi·a·ri mal·for·ma·tion

(ar'nŏld kē-ah'rē), [MIM*207950]
malformed posterior fossa structures associated with caudad traction and displacement of the rhombencephalon as caused by tethering of the spinal cord; may be accompanied in some cases by spina bifida and associated anomalies such as meningomyelocele; usually multifactorial in inheritance.
Farlex Partner Medical Dictionary © Farlex 2012

Arnold-Chiari malformation

A congenital compression deformity of the lower brain, which is characterised by herniation of the cerebellar tonsils and distal medulla oblongata through the foramen magnum into the spinal canal. The Arnold-Chiari malformation is accompanied by compression of the 4th ventricle and firm adhesions at the cisterna magna.
Segen's Medical Dictionary. © 2012 Farlex, Inc. All rights reserved.

Arnold-Chiari malformation

Neurology A congenital compression deformity of the 'lower brain' characterized by herniation of the cerebellar tonsils and distal medulla oblongata through the foramen magnum into the spinal canal; ACM is accompanied by compression of the 4th ventricle and firm adhesions at the cisterna magna
McGraw-Hill Concise Dictionary of Modern Medicine. © 2002 by The McGraw-Hill Companies, Inc.

Ar·nold-Chi·a·ri mal·for·ma·tion

(ahr'nŏld kē-ah'rē mal'fōr-mā'shŭn)
Deformity of posterior cranial fossa structures caused by tethering of the spinal cord with caudad traction and displacement of the rhombencephalon; may be accompanied by spina bifida and associated anomalies such as meningomyelocele; weak evidence of autosomal recessive inheritance.
Medical Dictionary for the Health Professions and Nursing © Farlex 2012

Arnold,

Julius, German pathologist, 1835-1915.
Arnold bodies - small portions or minute fragments of erythrocytes.
Arnold-Chiari deformity - Synonym(s): Arnold-Chiari malformation
Arnold-Chiari malformation - malformed posterior fossa structures. Synonym(s): Arnold-Chiari deformity; Arnold-Chiari syndrome; cerebellomedullary malformation syndrome
Arnold-Chiari syndrome - Synonym(s): Arnold-Chiari malformation

Chiari,

Hans, German pathologist, 1851-1916.
Arnold-Chiari deformity - Synonym(s): Arnold-Chiari malformation
Arnold-Chiari malformation - see under Arnold, Julius
Arnold-Chiari syndrome - Synonym(s): Arnold-Chiari malformation
Budd-Chiari syndrome - Synonym(s): Chiari syndrome
Chiari disease - Synonym(s): Chiari syndrome
Chiari net - abnormal fibrous or lacelike strands in the right atrium.
Chiari syndrome - thrombosis of the hepatic vein with great enlargement of the liver and extensive development of collateral vessels, intractable ascites, and severe portal hypertension. Synonym(s): Budd-Chiari syndrome; Budd syndrome; Chiari-Budd syndrome; Chiari disease; Rokitansky disease (2)
Chiari-Budd syndrome - Synonym(s): Chiari syndrome
Chiari II syndrome - elongation of medulla and cerebellar tonsils and vermis with displacement through the foramen magnum into the upper spinal canal.
Medical Eponyms © Farlex 2012
References in periodicals archive ?
Parent-reported executive dysfunction in children and adolescents with Chiari malformation type 1.
reported that childhood OSA syndrome has CSAs, and adenotonsillectomy leads to a significant decrease of both OSAs and CAI (and resolution of CSAs) [16], However, patients with medical conditions including neurological disorders and brain stem pathology such as CM1 may have increased CSAs [17], These disorders involve a disruption or dysfunction of breathing control in the central nervous system [18], likely due to the compression of the structures of the medulla that control the respiration [19], The relationship between increased central apnea index (CAI) and Chiari malformation is controversial [14, 19].
There are some differences in the management regarding to the order and the timing of the surgery in myelomeningocele associated with hydrocephalus and Chiari malformations. Here we discuss our management of a rare case of thoracic myelonmeningocele associated with hydrocephalus and Chiari type 2 malformation.
We report a case of Charcot elbow joint as the initial symptom in Chiari malformation with syringomyelia.
Normal 10.14% Hydrocephalus/ventriculomegaly 25.36% Chiari malformation 3.4% Dandy-Walker malformation 5.7% Holoprosencephaly 2.3% Intracranial masses Cysts 3.4% Microcephaly 1.1% Corpus callosum agenesis 6.9% Nonspecific 2.3% Soft-tissue masses 2.3% Hemivertebra 1.1% Diaphragmatic hernia 1.1% Cardiac rhabdomyoma 1.1 Pulmonary sequestration 1.1 Note: Table made from pie chart.
Let's shift our sights back to the abnormal anatomic features of Chiari malformation. In most cases, the posterior fossa is small, and neural elements are crowded and impacted at the foramen magnum.1 There was a time when lots of scholars acknowledging the crowding theory which postulated that restricted growth of the posterior fossa causes compression of neural tissue, which is then squeezed through the foramen magnum like toothpaste through a tube.5 In support of this theory, the posterior fossa is abnormally small and the torcula is displaced downward in patients with Chiari malformations.6 This is a kind of naive materialism and simple and dialectical view on the pathological theory of Chiari malformation.
His history revealed that he had a Chiari malformation and shunt surgery several years ago.
They address its anatomy and physiology, the neuropathology of human hydrocephalus, animal models, genetics, and epidemiology; the pathophysiology of gait dysfunction, cognitive dysfunction, and incontinence, as well as grading scales; diagnosis, differential diagnosis, imaging, monitoring, and cerebrospinal fluid biomarkers; treatment (shunt procedures and endoscopic third ventriculostomy), complications, and outcomes; and associated conditions like hemorrhage, infection, malignancy, cerebrospinal fluid leaks, congenital hydrocephalus, cerebrospinal fluid pathologies, Chiari malformation, and pseudotumor cerebri syndrome.
Natural history of Chiari malformation Type I following decision for conservative treatment.
LIAM shares the month with other causes, including National Guide Dog Month, National Honey Month, National Ovarian Cancer Awareness Month, Leukemia Awareness Month, National Prostate Cancer Awareness Month, National Preparedness Month and National Chiari Malformation Awareness Month.
Keywords: Arnold-Chiari malformation, Chiari malformation, hindbrain herniation, quality of life, syringomyelia, syrinx