Caroli syndrome

Ca·ro·li syn·drome

congenital malformation of the bile ducts within the liver leading to formation of multifocal cystic dilatations.

Ca·ro·li dis·ease

, Caroli syndrome (kah-rō-lē' di-zēz', sin'drōm)
Congenital cystic dilation of the intrahepatic bile ducts, sometimes associated with intrahepatic stones and biliary obstruction.
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References in periodicals archive ?
In our study, patients of Caroli syndrome were excluded because they were diagnosed on the basis of computed tomography (CT) scan of the abdomen and liver biopsies were not performed due to dilated biliary ducts.
5][7] The genetic basis for the difference between Caroli disease and Caroli syndrome has not been defined Disease affects about 1 in 1,000,000 people, with more reported cases of Caroli syndrome than of Caroli disease.
If both the large and small ducts are affected and both features of congenital hepatic fibrosis and Caroli disease are present, this entity is termed Caroli syndrome.