Caroli's disease

Hepatology A condition characterized by a diffuse distribution of intrahepatic biliary cysts and other cystic lesions–eg, medullary sponge kidneys Clinical Childhood onset–eg, jaundice, episodic fever, pain Complications Hepatic fibrosis, cirrhosis, portal HTN, esophageal bleeding, death in childhood

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CCA risk factors include, but are not limited to, primary sclerosing cholangitis, choledocholithiasis, long-standing ulcerative colitis, infestation with Clonorchis sinensis, Caroli's disease, and congenital hepatic fibrosis [2, 3, 8].

Intrahepatic Cholangiocarcinoma Masquerading as Acute Fatty Liver of Pregnancy: A Case Report and Review of the Literature

Shaikh, "Caroli's disease and liver transplantation," Liver Transplantation, vol.

Severe Hepatopulmonary Syndrome in a Child with Caroli Syndrome

The cholangitis form of CHF is also defined in the literature and differentiation from Caroli's disease is difficult.

Congenital hepatic fibrosis: clinical presentation, laboratory features and management at a tertiary care hospital of Lahore

Son Marley, six, is her inspiration, as he continues to bravely fight liver and kidney diseases portal hypertension, congenital hepatic fibrosis, Caroli's disease and polycystic kidney disease.

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Risk factors of cholangiocarcinogenesis, after Ghouri et al [2] Primary sclerosing cholangitis Hepatolithiasis Liver flukes--Opistorchis vierrini and Clonorchis sinensis Caroli's disease Congenital hepatic fibrosis Viral hepatitis B and C infection Liver cirrhosis Obesity and diabetes Chemical compounds--dioxin, thorotrast Choledocal cysts

Over 6-year survival in locally advanced cholangiocarcinoma--a case report

Other factors associated with increased risk include Caroli's disease, biliary ascariasis, and biliary tract surgery.

Ruptured liver abscess: an unusual cause of pneumoperitoneum

The role of surgery in Caroli's disease. J Am Coll Surg.

Confidently characterizing benign liver tumors

Caroli's disease with hepatolithiasis and cholangiocarcinoma.

Imaging of a patient with multiple intrahepatic cysts

The differential diagnosis includes simple cysts, echinococcal cysts, liver abscesses, cystic degeneration of a liver neoplasm, Caroli's disease, posttraumatic cysts, and polycystic diseases.

Mucinous cystic neoplasm of the liver: mimicker of echinococcal cyst

Finally, type D, Caroli's disease, represents Todani V, which is a ductal plate anomaly and is associated with congenital hepatic fibrosis.

Cystic lesions of the biliary tree: proposal for a revised classification system

Autosomal dominant polycystic kidney disease (ADPKD) is the most common inherited disorder of the kidney and the third most common cause of end-stage renal disease (ESRD).[sup.1] It is characterized by bilaterally enlarged kidneys containing multiple cysts.[sup.2] Caroli's disease is a much less frequent condition in which there is ectasia of the intrahepatic bile ducts.[sup.3] There is a well-established association between autosomal recessive polycystic kidney disease (ARPKD) and Caroli's disease,[sup.4] but only 4 case reports of ADPKD and Caroli's disease, with 2 reported postoperative mortalities (Table 1).

Nephrectomy in patients with Caroli's and ADPKD may be associated with increased morbidity

Algino, who is nine years old, was diagnosed with Caroli's disease in 2005 and needs to undergo a liver transplant operation in Germany.