CCA risk factors include, but are not limited to, primary sclerosing cholangitis, choledocholithiasis, long-standing ulcerative colitis, infestation with Clonorchis sinensis, Caroli's disease
, and congenital hepatic fibrosis [2, 3, 8].
Shaikh, "Caroli's disease
and liver transplantation," Liver Transplantation, vol.
The cholangitis form of CHF is also defined in the literature and differentiation from Caroli's disease
Son Marley, six, is her inspiration, as he continues to bravely fight liver and kidney diseases portal hypertension, congenital hepatic fibrosis, Caroli's disease
and polycystic kidney disease.
Risk factors of cholangiocarcinogenesis, after Ghouri et al  Primary sclerosing cholangitis Hepatolithiasis Liver flukes--Opistorchis vierrini and Clonorchis sinensis Caroli's disease
Congenital hepatic fibrosis Viral hepatitis B and C infection Liver cirrhosis Obesity and diabetes Chemical compounds--dioxin, thorotrast Choledocal cysts
Other factors associated with increased risk include Caroli's disease
, biliary ascariasis, and biliary tract surgery.
The role of surgery in Caroli's disease
. J Am Coll Surg.
with hepatolithiasis and cholangiocarcinoma.
The differential diagnosis includes simple cysts, echinococcal cysts, liver abscesses, cystic degeneration of a liver neoplasm, Caroli's disease
, posttraumatic cysts, and polycystic diseases.
Finally, type D, Caroli's disease
, represents Todani V, which is a ductal plate anomaly and is associated with congenital hepatic fibrosis.
Autosomal dominant polycystic kidney disease (ADPKD) is the most common inherited disorder of the kidney and the third most common cause of end-stage renal disease (ESRD).[sup.1] It is characterized by bilaterally enlarged kidneys containing multiple cysts.[sup.2] Caroli's disease
is a much less frequent condition in which there is ectasia of the intrahepatic bile ducts.[sup.3] There is a well-established association between autosomal recessive polycystic kidney disease (ARPKD) and Caroli's disease
,[sup.4] but only 4 case reports of ADPKD and Caroli's disease
, with 2 reported postoperative mortalities (Table 1).
Algino, who is nine years old, was diagnosed with Caroli's disease
in 2005 and needs to undergo a liver transplant operation in Germany.