Caroli's disease

Caroli's disease

Hepatology A condition characterized by a diffuse distribution of intrahepatic biliary cysts and other cystic lesions–eg, medullary sponge kidneys Clinical Childhood onset–eg, jaundice, episodic fever, pain Complications Hepatic fibrosis, cirrhosis, portal HTN, esophageal bleeding, death in childhood
References in periodicals archive ?
CCA risk factors include, but are not limited to, primary sclerosing cholangitis, choledocholithiasis, long-standing ulcerative colitis, infestation with Clonorchis sinensis, Caroli's disease, and congenital hepatic fibrosis [2, 3, 8].
Shaikh, "Caroli's disease and liver transplantation," Liver Transplantation, vol.
The cholangitis form of CHF is also defined in the literature and differentiation from Caroli's disease is difficult.
Son Marley, six, is her inspiration, as he continues to bravely fight liver and kidney diseases portal hypertension, congenital hepatic fibrosis, Caroli's disease and polycystic kidney disease.
Risk factors of cholangiocarcinogenesis, after Ghouri et al [2] Primary sclerosing cholangitis Hepatolithiasis Liver flukes--Opistorchis vierrini and Clonorchis sinensis Caroli's disease Congenital hepatic fibrosis Viral hepatitis B and C infection Liver cirrhosis Obesity and diabetes Chemical compounds--dioxin, thorotrast Choledocal cysts
Other factors associated with increased risk include Caroli's disease, biliary ascariasis, and biliary tract surgery.
The role of surgery in Caroli's disease. J Am Coll Surg.
Caroli's disease with hepatolithiasis and cholangiocarcinoma.
The differential diagnosis includes simple cysts, echinococcal cysts, liver abscesses, cystic degeneration of a liver neoplasm, Caroli's disease, posttraumatic cysts, and polycystic diseases.
Finally, type D, Caroli's disease, represents Todani V, which is a ductal plate anomaly and is associated with congenital hepatic fibrosis.
Autosomal dominant polycystic kidney disease (ADPKD) is the most common inherited disorder of the kidney and the third most common cause of end-stage renal disease (ESRD).[sup.1] It is characterized by bilaterally enlarged kidneys containing multiple cysts.[sup.2] Caroli's disease is a much less frequent condition in which there is ectasia of the intrahepatic bile ducts.[sup.3] There is a well-established association between autosomal recessive polycystic kidney disease (ARPKD) and Caroli's disease,[sup.4] but only 4 case reports of ADPKD and Caroli's disease, with 2 reported postoperative mortalities (Table 1).
Algino, who is nine years old, was diagnosed with Caroli's disease in 2005 and needs to undergo a liver transplant operation in Germany.