ALDH7A1

(redirected from Betaine aldehyde dehydrogenase)

ALDH7A1

A gene on chromosome 5q31 that encodes an aldehyde dehydrogenase involved in lysine catabolism in the mitochondrial matrix.

Molecular pathology
ALDH7A1 mutation are associated with pyridoxine-dependent epilepsy.
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(2008) who stated that the presence of dominant Badh2 allele encoding Betaine Aldehyde Dehydrogenase (BADH2) inhibited synthesis of 2AP, while its recessive alleles induced 2AP formation.
Badh2, encoding betaine aldehyde dehydrogenase, inhibits the biosynthesis of 2-Acetyl-1-pyrroline, a major component in rice fragrance.
The effect of salt on betaine aldehyde dehydrogenase transcript levels and 2-Acetyl-1-pyrroline concentration in fragrant and non-fragrant rice (Oryza sativa, L.).
By conversion of choline to betaine by betaine aldehyde dehydrogenase and choline dehydrogenase [11], the three methyl groups of choline are readily available for three different conversions: (1) sarcosine into glycine by sarcosine dehydrogenase enzyme, (2) by using betaine from betaine-homocysteine methyltransferase as methyl donor and converting homocysteine into methionine, and (3) in conversion of dimethylglycine into sarcosine by dimethylglycine dehydrogenase enzyme.
Betaine is synthesized by a two-step oxidation of choline in which mitochondrial choline oxidase first catalyzes the production of betaine aldehyde, which is further oxidized by mitochondrial betaine aldehyde dehydrogenase to betaine (Dragolovich, 1994).
Transformation of wheat with a gene encoding for the betaine aldehyde dehydrogenase (BADH).
The Suaeda liaotungensis kitag betaine aldehyde dehydrogenase gene improves salt tolerance of transgenic maize mediated with minimum linear length of DNA fragment.
Choline monooxygenase (CMO), which catalyzes the oxidation of choline to betaine aldehyde, and betaine aldehyde dehydrogenase (BADH), which oxidizes betaine aldehyde to GB, are both induced under osmotic stress (Hanson et al., 1985; Ishitani et al., 1995; Rathinasabapathi et al., 1997).
Expression of the betaine aldehyde dehydrogenase gene in barley in response to osmotic stress and abscisic acid.
Characterization of betaine aldehyde dehydrogenase from Cylindrocarpon didymum M-1.
Purification and properties of betaine aldehyde dehydrogenase from Xanthomonas translucens.
Purification and properties of betaine aldehyde dehydrogenase with high affinity for NADP from Arthrobacter globiformis.