Behcet syndrome


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Beh·çet syn·drome

(be-shet'), [MIM*109650]
a syndrome characterized by simultaneously or successively occurring recurrent attacks of genital and oral ulcerations (aphthae) and uveitis or iridocyclitis with hypopyon, often with arthritis; a phase of a generalized disorder, occurring more often in men than in women, with variable manifestations, including dermatitis, erythema nodosum, thrombophlebitis, and cerebral involvement.

Beh·çet syn·drome

, Behçet disease (beh-chet' sin'drōm, di-zēz')
A syndrome characterized by simultaneously or successively occurring recurrent attacks of genital and oral ulcerations (aphthae) and uveitis or iridocyclitis with hypopyon, often with arthritis; a phase of a generalized disorder, occurring more often in men than in women, with variable manifestations, including dermatitis, erythema nodosum, thrombophlebitis, and cerebral involvement.
Synonym(s): uveoencephalitic syndrome.

Behçet,

Hulusi, Turkish dermatologist, 1889-1948.
Adamantiades-Behçet syndrome - Synonym(s): Behçet syndrome
Behçet disease - Synonym(s): Behçet syndrome
Behçet syndrome - severe uveitis with ulceration of mouth and genitalia. Synonym(s): Adamantiades-Behçet syndrome; Behçet disease; cutaneomucouveal syndrome; iridocyclitis septica; recurrent hypopyon; triple symptom complex

Beh·çet syn·drome

(be-shet sindrōm) [MIM*109650]
Syndrome characterized by simultaneously or successively occurring recurrent attacks of genital and oral ulcerations (aphthae) and uveitis or iridocyclitis with hypopyon, often with arthritis.
References in periodicals archive ?
Similar to that of most diseases, genetic and environmental factors participate in the pathogenesis of Behcet syndrome. The exact contribution of these factors to the emergence of Behcet disease, however, is unknown.
Given that patients with Behcet syndrome have heterogeneous clinical expressions and universal diagnostic criteria for Behcet disease do not exist, I used the International Study Group Criteria for Behcet Disease criteria to standardize the study group (3).
It is mostly idiopathic; nevertheless, underplaying immunological anomalies have been recognized.2 Fifty percent of the patients have underlying systemic diseases such as inflammatory bowel diseases, polyarthritis, diverticulosis, paraproteinaemia, myeloma, leukaemia, active chronic hepatitis, and Behcet syndrome.1 There are four known variants of pyoderma gangrenosum; ulcerative, pustular, bullous and superficial.3
Pulmonary artery aneurysms in Behcet syndrome. Am J Med 2004;117:867-70.
Saip et al., "Thalidomide in the treatment of the mucocutaneous lesions of the Behcet syndrome: a randomized, double-blind, placebo-controlled trial," Annals of Internal Medicine, vol.
There is currently no curative treatment for Behcet syndrome and treatment is directed against preventing irreversible organ damage.
Evaluation and therapeutic approaches of voiding and erectile dysfunction in neurological Behcet syndrome. J Urol 1999;162:147-5.
Behcet syndrome is an autoimmune, multisystemic disease of unknown etiology.
Behcet syndrome manifestations and activity in the United States versus Turkey--a cross-sectional cohort comparison.
Seyahi et al., "The long-term mortality and morbidity of Behcet syndrome: a 2-decade outcome survey of 387 patients followed at a dedicated center," Medicine, vol.
Topiramate-responsive headache due to intracranial hypertension in Behcet syndrome. Headache 2004;44:436-437.