autoimmune lymphoproliferative syndrome


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autoimmune lymphoproliferative syndrome

A condition caused by defective lymphocyte homeostasis and characterised by:
• Non-malignant lymphoproliferation (lymphadenopathy, hepatosplenomegaly with or without hypersplenism) that often improves with age;
• Autoimmune disease, mostly directed toward peripheral blood cells; and
• Lifelong increased risk of Hodgkin and non-Hodgkin lymphoma.
References in periodicals archive ?
Identifying autoimmune lymphoproliferative syndrome in children with Evans syndrome: a multi-institutional study.
Advances in the management and understanding of autoimmune lymphoproliferative syndrome (ALPS).

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