auditory neuropathy


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auditory neuropathy

a disorder of hearing in children characterized by sensorineural hearing loss for pure tones, reduced word discrimination disproportionate to the pure tone loss, normal outer hair cell function as determined by measurement of otoacoustic emissions, and absent or abnormal auditory brainstem response.

au·di·to·ry neu·rop·a·thy

(aw'di-tōr-ē nūr-op'ă-thē)
A distinctive type of hearing deficit that seemingly is due to a malfunction of the eighth cranial nerve. Previously referred to as auditory neural synchrony disorder. Speech comprehension in quiet surroundings is out of proportion to the pure tone threshold elevation.

auditory neuropathy

Abbreviation: AN
Impaired hearing in children due to an absence of auditory evoked potentials, despite the presence of normal cochlear hair cell structure and function.
Synonym: auditory dyssynchrony
See also: neuropathy
References in periodicals archive ?
Pathophysiological mechanisms and functional hearing consequences of auditory neuropathy.
Unilateral auditory neuropathy spectrum disorder: retrocochlear lesion in disguise?
Central auditory maturation and behavioral outcome in children with auditory neuropathy spectrum disorder who use cochlear implants.
Variation in Auditory Neuropathy Spectrum Disorder: Implications for Evaluation and Management.
A novel missense mutation in a C2 domain of oToF results in autosomal recessive auditory neuropathy.
Since we previously knew of only two genes associated with auditory neuropathy, finding this gene mutation is significant.
Cochlear microphonics was observed which reversed with change in polarity of stimuli suggestive of auditory neuropathy (Fig 6, 7).
RESULTS: A child with hard of hearing and inability to speak with negligible or very abnormal brainstem evoked response reading together with a normal otoacoustic emission reading suggestive of auditory neuropathy.