Honeycomb Atrophy

(redirected from Atrophoderma Vermiculatum)
A rare autosomal recessive [MIM 209700] symmetric dermatopathy (genodermatosis) characterised by skin atrophy with sharply demarcated ‘pits’, variably accompanied by cardiac defects, mental retardation, neurofibromas.
Prognosis Usually slowly progressive; spontaneous regression has been reported.
Management Dermabrasion, cryotherapy, ultraviolet light radiation, topical medications, CO2 and 585 nm pulsed dye lasers
Segen's Medical Dictionary. © 2012 Farlex, Inc. All rights reserved.
References in periodicals archive ?
Papules and cysts around the elbow, pitted scars over the healed lesions, atrophoderma vermiculatum and hypo pigmented streaks over the scalp can be associated with APL (7).
Atrichia with papular lesions--a case report
Differential diagnoses included scarring secondary to varicella, atrophoderma vermiculatum, hydroa vacciniforme and infantile acne but these were excluded by the chronic course, clinical findings and lack of seasonal variation.
Atrophia maculosa varioliformis cutis - a rare case report
Generalized BFH may represent generalized follicular hamartoma syndrome (Brown-Crounse syndrome), tuberous sclerosis, Cowden syndrome ("multiple hamartoma syndrome" involving organs from all 3 germinal layers), multiple trichoepitheliomas, NBCCS, Rombo syndrome (atrophoderma vermiculatum of the face, multiple milia, telangiectases, acral erythema, and a propensity to develop BCC), and multiple tumors of the follicular infundibulum.
Basaloid follicular hamartoma
Medical browser ?
Full browser ?