Arnold-Chiari malformation


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Related to Arnold-Chiari malformation: Dandy-Walker syndrome, Dandy-Walker malformation

Ar·nold-Chi·a·ri mal·for·ma·tion

(ar'nŏld kē-ah'rē), [MIM*207950]
malformed posterior fossa structures associated with caudad traction and displacement of the rhombencephalon as caused by tethering of the spinal cord; may be accompanied in some cases by spina bifida and associated anomalies such as meningomyelocele; usually multifactorial in inheritance.

Arnold-Chiari malformation

A congenital compression deformity of the lower brain, which is characterised by herniation of the cerebellar tonsils and distal medulla oblongata through the foramen magnum into the spinal canal. The Arnold-Chiari malformation is accompanied by compression of the 4th ventricle and firm adhesions at the cisterna magna.

Arnold-Chiari malformation

Neurology A congenital compression deformity of the 'lower brain' characterized by herniation of the cerebellar tonsils and distal medulla oblongata through the foramen magnum into the spinal canal; ACM is accompanied by compression of the 4th ventricle and firm adhesions at the cisterna magna

Ar·nold-Chi·a·ri mal·for·ma·tion

(ahr'nŏld kē-ah'rē mal'fōr-mā'shŭn)
Deformity of posterior cranial fossa structures caused by tethering of the spinal cord with caudad traction and displacement of the rhombencephalon; may be accompanied by spina bifida and associated anomalies such as meningomyelocele; weak evidence of autosomal recessive inheritance.

Arnold,

Julius, German pathologist, 1835-1915.
Arnold bodies - small portions or minute fragments of erythrocytes.
Arnold-Chiari deformity - Synonym(s): Arnold-Chiari malformation
Arnold-Chiari malformation - malformed posterior fossa structures. Synonym(s): Arnold-Chiari deformity; Arnold-Chiari syndrome; cerebellomedullary malformation syndrome
Arnold-Chiari syndrome - Synonym(s): Arnold-Chiari malformation

Chiari,

Hans, German pathologist, 1851-1916.
Arnold-Chiari deformity - Synonym(s): Arnold-Chiari malformation
Arnold-Chiari malformation - see under Arnold, Julius
Arnold-Chiari syndrome - Synonym(s): Arnold-Chiari malformation
Budd-Chiari syndrome - Synonym(s): Chiari syndrome
Chiari disease - Synonym(s): Chiari syndrome
Chiari net - abnormal fibrous or lacelike strands in the right atrium.
Chiari syndrome - thrombosis of the hepatic vein with great enlargement of the liver and extensive development of collateral vessels, intractable ascites, and severe portal hypertension. Synonym(s): Budd-Chiari syndrome; Budd syndrome; Chiari-Budd syndrome; Chiari disease; Rokitansky disease (2)
Chiari-Budd syndrome - Synonym(s): Chiari syndrome
Chiari II syndrome - elongation of medulla and cerebellar tonsils and vermis with displacement through the foramen magnum into the upper spinal canal.
References in periodicals archive ?
(4-6) Arnold-Chiari malformations, post-traumatic syringomyelia, cervical spondylosis, infection, and diabetes are other potential causes.
Key words: Cough headache, Arnold-Chiari malformation type 1, topiramate
Multiple structural abnormalities of the spinal cord and brain have been described in patients with MVSD including cerebral polygyria, (7) diastematomyelia, (8) Arnold-Chiari malformation with thoracolumbar meningomyelocele, (9) thoracolumbar rachischisis5 and hydrocephalus due to aqueductal stenosis, spina bifida cystica in the thoracolumbar region, and diastematomyelia.
[27.] Saez R, Onofrio B, Yanagihara T: Experience with Arnold-Chiari malformation, 1960-1970.
Arnold-Chiari malformation is a congenital disorder manifesting in late adulthood.
Positional nystagmus has been reported in patients with a cerebellopontine angle tumor, Arnold-Chiari malformation, multiple sclerosis, lateral medullary infarction, or brainstem contusion.
See: Arnold-Chiari Malformation, Joubert Syndrome, Syringomyelia
Anesthetic management of a child with Arnold-Chiari malformation and Klippel-Feil syndrome.
Neurologic disorders such as Arnold-Chiari malformation, myotonic dystrophy, pseudobulbar palsy, pharyngeal paresis, myasthenia gravis, and neurofibromatosis
Anesthetic management during Cesarean section in a woman with residual Arnold-Chiari malformation Type I, cervical kyphosis, and syringomyelia.
The iter (or top of the cerebral aqueduct) typically descends below the incisural line, as opposed to Arnold-Chiari malformations where the iter typically remains unchanged in position (Figure 2).
Fetal Indications: Thalassaemia (1.86%), Congenital heart defect (1.86%), Hydropsfetalis (1.86%), Meningoencephalocele (1.40%), Dysplastic kidney (1.40%), Polycystic kidney (0.93%), Renal agenesis (0.93%), deformed Twin pregnancy (0.93%), Dysplastic chest (0.47%), Esophageal atresia (0.47%), Arnold-Chiari Malformations (0.47%), Dilated lateral ventricles (0.47%), Hydronephrosis (0.47%).