Percutaneous coronary intervention in infants remains rare with only four prior cases reported in
ALCAPA patients [3-6].
In infants and children with
ALCAPA, a false initial diagnosis at different ages occurs frequently owing to the lack of specificity in the clinical manifestations, which range from asymptomatic to severe myocardial ischemia, heart failure, and sudden death.[2] The area and extent of myocardial infarction may decide the clinical manifestations and outcome.
She underwent surgery for atrial septal defect at 10 years of age and the repair of suspected right coronary artery (RCA) fistula into the right ventricle according to cardiac catheterization, while the
ALCAPA was not detected.
The diagnosis of
ALCAPA was impressed, and surgical treatment was advised.
The advanced development in cardiac CT and magnetic resonance imaging (MRI) provides noninvasive diagnostic tools for
ALCAPA. Multislice computed tomography (MSCT) is a non-invasive imaging tool, and it has an excellent spatial resolution that allows excellent evaluation of small coronary arteries.
Sell, who has repaired more than a dozen cases of
ALCAPA in children and several in adults, is one of the most experienced surgeons in the world treating the rare and complex heart defect.
Catheterization-angiography was decided to be performed considering
ALCAPA as a result of echocardiographic examination.
There are two types of
ALCAPA syndrome: the adult and the infant type.
The news comes as an inquest into Maddie's death, held yesterday, heard how a combination of pneumonia and the 18-month-old's undetected heart defect, called
Alcapa (Anomalous left coronary artery from the pulmonary artery), caused her life to be tragically cut short.
Doctors were later to tell Anna, Maddie's dad Martin Butterfield, 30, and little sister Codie, seven, the youngster was suffering from the heart defect
Alcapa (Anomalous left coronary artery from the pulmonary artery), a rare condition near-impossible to detect until it's too late.
Principal structural elements of the Outer Carpathians fold-and-thrust belt were shaped in the Palaeogene and Neogene, when the study area represented an accretionary prism associated with the south-directed subduction of the European Platform under the
ALCAPA block (Tomek and Hall, 1993; Oszczypko, 1998, 2001; Fodor et al., 1999).
ALCAPA is a rare congenital cardiovascular malformation in which the left coronary artery originates from the pulmonary artery (PA) instead of the left coronary sinus [1].