ALCAPA


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ALCAPA

Anomalous origin of the left coronary artery from the pulmonary artery. A rarely identified congenital cardiac defect which presents in adulthood as malignant ventricular arrhythmias and sudden cardiac death.
Management Re-routing of the coronary arteries; cryotherapy to treat the ventricular tachycardia.
References in periodicals archive ?
Percutaneous coronary intervention in infants remains rare with only four prior cases reported in ALCAPA patients [3-6].
In infants and children with ALCAPA, a false initial diagnosis at different ages occurs frequently owing to the lack of specificity in the clinical manifestations, which range from asymptomatic to severe myocardial ischemia, heart failure, and sudden death.[2] The area and extent of myocardial infarction may decide the clinical manifestations and outcome.
She underwent surgery for atrial septal defect at 10 years of age and the repair of suspected right coronary artery (RCA) fistula into the right ventricle according to cardiac catheterization, while the ALCAPA was not detected.
The advanced development in cardiac CT and magnetic resonance imaging (MRI) provides noninvasive diagnostic tools for ALCAPA. Multislice computed tomography (MSCT) is a non-invasive imaging tool, and it has an excellent spatial resolution that allows excellent evaluation of small coronary arteries.
Sell, who has repaired more than a dozen cases of ALCAPA in children and several in adults, is one of the most experienced surgeons in the world treating the rare and complex heart defect.
Catheterization-angiography was decided to be performed considering ALCAPA as a result of echocardiographic examination.
There are two types of ALCAPA syndrome: the adult and the infant type.
The news comes as an inquest into Maddie's death, held yesterday, heard how a combination of pneumonia and the 18-month-old's undetected heart defect, called Alcapa (Anomalous left coronary artery from the pulmonary artery), caused her life to be tragically cut short.
Doctors were later to tell Anna, Maddie's dad Martin Butterfield, 30, and little sister Codie, seven, the youngster was suffering from the heart defect Alcapa (Anomalous left coronary artery from the pulmonary artery), a rare condition near-impossible to detect until it's too late.
Principal structural elements of the Outer Carpathians fold-and-thrust belt were shaped in the Palaeogene and Neogene, when the study area represented an accretionary prism associated with the south-directed subduction of the European Platform under the ALCAPA block (Tomek and Hall, 1993; Oszczypko, 1998, 2001; Fodor et al., 1999).
ALCAPA is a rare congenital cardiovascular malformation in which the left coronary artery originates from the pulmonary artery (PA) instead of the left coronary sinus [1].