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Systemic vasculitis |
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systemic vasculitis Noninfectious vasculitis Vascular disease Any of a number of conditions characterized by inflammation of vessels in multiple sites in the body, which share many clinical and lab features Clinical Fever, fatigue, anorexia,
weight loss, polymyalgia rheumatica, nondestructive oligoarthritis Lab ↑ ESR, anemia, thrombocytosis, ↓ albumin Pathogenesis Unknown Management Corticosteroids, cytotoxic agents; the various forms of SV have been formally classified by the
Chapel Hill Consensus Conference according to size–small, medium-sized, large, and the major forms defined. See Vasculitis.
Systemic vasculitis
Large vessel vasculitis
Giant cell (temporal) arteritis
Takayasu's arteritis
Medium-sized vessel vasculitis
Polyarteritis nodosa
Kawasaki's disease
Primary granulomatous CNS vasculitis
Small vessel vasculitis
ANCA-associated small vessel vasculitis
Churg-Strauss syndrome
Drug-induced ANCA-associated vasculitis
Microscopic polyangiitis
Wegener's granulomatosis
Immune complex small vessel vasculitis
Behçet's disease
Cryoglobulinemic vasculitis
Drug-induced immune complex vasculitis
Goodpasture syndrome
Henoch-Schönlein purpura
Hypocomplementemic urticarial vasculitis
Infection-induced immune complex vasculitis
Lupus vasculitis
Rheumatoid vasculitis
Serum sickness vasculitis
Sjögren syndrome vasculitis
Paraneoplastic small vessel vasculitis
Carcinoma-induced vasculitis
Lymphoproliferative neoplasm-induced vasculitis
Myeloproliferative neoplasm-induced vasculitis
Inflammatory bowel disease vasculitis
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