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Systemic vasculitis

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systemic vasculitis
Noninfectious vasculitis Vascular disease Any of a number of conditions characterized by inflammation of vessels in multiple sites in the body, which share many clinical and lab features Clinical Fever, fatigue, anorexia, weight loss, polymyalgia rheumatica, nondestructive oligoarthritis Lab ↑ ESR, anemia, thrombocytosis, ↓ albumin Pathogenesis Unknown Management Corticosteroids, cytotoxic agents; the various forms of SV have been formally classified by the Chapel Hill Consensus Conference according to size–small, medium-sized, large, and the major forms defined. See Vasculitis.
Systemic vasculitis  
Large vessel vasculitis  
Giant cell (temporal) arteritis
 Takayasu's arteritis
Medium-sized vessel vasculitis  
Polyarteritis nodosa
 Kawasaki's disease
 Primary granulomatous CNS vasculitis
Small vessel vasculitis  
ANCA-associated small vessel vasculitis
 Churg-Strauss syndrome
 Drug-induced ANCA-associated vasculitis
 Microscopic polyangiitis
 Wegener's granulomatosis
 Immune complex small vessel vasculitis
 Behçet's disease
 Cryoglobulinemic vasculitis
 Drug-induced immune complex vasculitis
 Goodpasture syndrome
 Henoch-Schönlein purpura
 Hypocomplementemic urticarial vasculitis
 Infection-induced immune complex vasculitis
 Lupus vasculitis
 Rheumatoid vasculitis
 Serum sickness vasculitis
 Sjögren syndrome vasculitis
 Paraneoplastic small vessel vasculitis
  Carcinoma-induced vasculitis
  Lymphoproliferative neoplasm-induced vasculitis
  Myeloproliferative neoplasm-induced vasculitis
 Inflammatory bowel disease vasculitis


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