systemic vasculitis

systemic vasculitis

Noninfectious vasculitis Vascular disease Any of a number of conditions characterized by inflammation of vessels in multiple sites in the body, which share many clinical and lab features Clinical Fever, fatigue, anorexia, weight loss, polymyalgia rheumatica, nondestructive oligoarthritis Lab ↑ ESR, anemia, thrombocytosis, ↓ albumin Pathogenesis Unknown Management Corticosteroids, cytotoxic agents; the various forms of SV have been formally classified by the Chapel Hill Consensus Conference according to size–small, medium-sized, large, and the major forms defined. See Vasculitis.
Systemic vasculitis  
Large vessel vasculitis  
Giant cell (temporal) arteritis
 Takayasu's arteritis
Medium-sized vessel vasculitis  
Polyarteritis nodosa
 Kawasaki's disease
 Primary granulomatous CNS vasculitis
Small vessel vasculitis  
ANCA-associated small vessel vasculitis
 Churg-Strauss syndrome
 Drug-induced ANCA-associated vasculitis
 Microscopic polyangiitis
 Wegener's granulomatosis
 Immune complex small vessel vasculitis
 Behçet's disease
 Cryoglobulinemic vasculitis
 Drug-induced immune complex vasculitis
 Goodpasture syndrome
 Henoch-Schönlein purpura
 Hypocomplementemic urticarial vasculitis
 Infection-induced immune complex vasculitis
 Lupus vasculitis
 Rheumatoid vasculitis
 Serum sickness vasculitis
 Sjögren syndrome vasculitis
 Paraneoplastic small vessel vasculitis
  Carcinoma-induced vasculitis
  Lymphoproliferative neoplasm-induced vasculitis
  Myeloproliferative neoplasm-induced vasculitis
 Inflammatory bowel disease vasculitis
References in periodicals archive ?
Systemic vasculitis was diagnosed by the Chapel Hill consensus criteria (9).
Patients with ANCA-associated systemic vasculitis (AAV) including MPA may have antibodies which cross-react with pathogen antigens, and may be involved in the pathogenesis of this disease.
Behcet's Disease, sometimes called Behcet's syndrome, or Morbus Behcet, Behcet-Adamantiades syndrome, or Silk Road disease, is a rare immune-mediated small-vessel systemic vasculitis that often presents with mucous membrane ulceration and ocular problems.
An extensive workup for systemic vasculitis was negative, including antinuclear antibody, double-stranded DNA, serum complement, rheumatoid factor, anticardiolipin, anti SS-A and SS-B, anticentromere, antiScl-70, anti-C3, and anti-myeloperoxidase antibodies (Table 1).
Sequential development of systemic vasculitis with anti-neutrophil cytoplasmic antibodies complicating anti-glomerular basement membrane disease.
Although pulmonary capillaritis is a histopathologic diagnosis that is not pathognomonic of a specific disorder, its presence typically raises the possibility of an underlying systemic vasculitis or collagen vascular disease.
Although other causes such as coronary artery emboli, dissection, cocaine toxicity, congenital coronary anomalies, systemic vasculitis, metabolic and hematologic disorders are rare, they should be envisaged in the differential diagnosis in patients with systemic symptoms or atypical involvement of the vessels and in young patients.
When the health condition of the patient worsened due to the incorrect treatment being given, he was moved to another hospital, where his condition was diagnosed as Behcet's disease -- a rare immune-mediated small-vessel systemic vasculitis that can cause ocular problems.
MPA is a small vessel vasculitis according to the Chapel-Hill Consensus Conference on the nomenclature of systemic vasculitis establishing the names and definitions of many vasculities that affect the kidneys (1).
In addition, Euro Diagnostica has been the first to develop anti-neutrophil cytoplasmic antibodies (ANCA) tests for diagnosing systemic vasculitis and related diseases.
Less common associations with a range of other conditions have also been reported, including juvenile rheumatoid arthritis, systemic vasculitis, Vogt-Koyanagi-Harada disease, sarcoidosis and lymphoma.

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