sclerodactyly


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Related to sclerodactyly: calcinosis, acroosteolysis

sclerodactyly

 [skle″ro-dak´tĭ-le]
scleroderma of the fingers and toes.

ac·ro·scle·ro·sis

(ak'rō-sklĕ-rō'sis),
Stiffness and tightness of the skin of the fingers, with atrophy of the soft tissue and osteoporosis of the distal phalanges of the hands and feet; a limited form of progressive systemic sclerosis occurring with Raynaud phenomenon and scleroderma of the forearms. See: CREST syndrome.

sclerodactyly

/scle·ro·dac·ty·ly/ (-dak´tĭ-le) localized scleroderma of the digits.

sclerodactyly

[sklir′ōdak′tilē]
Etymology: Gk, skleros + daktylos, finger
a musculoskeletal deformity affecting the hands of people with scleroderma. The fingers are fixed in a semiflexed position, with subcutaneous calcification and tightened skin to the wrist. The fingertips may be ulcerated.
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Sclerodactyly

ac·ro·scle·ro·sis

(ak'rō-skler-ō'sis)
Stiffness and tightness of the skin of the fingers, with atrophy of the soft tissue and osteoporosis of the distal phalanges of the hands and feet; a limited form of progressive systemic sclerosis occurring with Raynaud phenomenon.
See: CREST syndrome
Synonym(s): sclerodactyly, sclerodactylia.
References in periodicals archive ?
Physical examination and imaging studies revealed Raynaud's phenomenon, stellate scars, sclerodactyly, pulmonary fibrosis, pulmonary hypertension, and cardiac arrhythmias in a majority of patients (Table 1).
Over time, repeated bouts of Raynaud's phenomenon, in addition to the aforementioned pathologic features of CREST, lead to tissue fibrosis causing characteristic sclerodactyly (loss of the digital pad) or may lead to digital ulceration descriptively termed "rat bite necrosis.
Now, sclerodactyly means basically hardening of the skin.
Similarly, our patient suffered from skin flattening, slimness, color change with sclerodactyly and difficulty in opening his mouth, and tight lip skin.
Other risk factors include severe Raynaud's phenomenon, low pulmonary diffusing capacity, and the calcinosis, Raynaud's disease, esophageal dysmotility, sclerodactyly, and telangiectasia (CREST) syndrome, he said.
Examination was remarkable for normal optic fundi, multiple small telangiectasias on her face, diminished breath sounds at both lung bases with coarse crackles; her extremities were remarkable for swelling of both hands with sclerodactyly.
Hence, systemic lupus erythematosus, discoid lupus erythematosus, scleroderma/CREST (calcinosis, Raynaud phenomenon, esophageal motility abnormalities, sclerodactyly, and telangiectasia), Raynaud syndrome, SS, MCTD, overlap CTD syndromes, polymyositis, and dermatomyositis were considered disease-positive [11] and all other diagnoses were considered disease-negative.
1) Raynaud's phenomenon, joint involvement, sclerodactyly, and constitutional symptoms found in scleroderma are not present in morphea.
ANA subtypes (a) Patterns Disease association Anti-double-stranded DNA Highly specific, but not sensitive for SLE (peripheral) Anti-Smith (speckled) Highly specific, but not sensitive for SLE Anti-Ro (speckled) SLE, SS, neonatal SLE Anti-La (speckled) SLE, SS, neonatal SLE Antihistone (diffuse) SLE, RA, aging, DILE Anti-RNP (speckled) SLE, MCTD Anticentromere Limited scleroderma (CREST syndrome) (a) ANA, antinuclear antibody; SLE, systemic lupus erythematosus; SS, Sjogrens syndrome; RA, rheumatoid arthritis; DILE, drug-induced lupus erythematosus; RNP, ribo-nuclear protein; MCTD, mixed connective tissue disease; CREST, calcinosis, Raynauds, esophageal dysfunction, sclerodactyly, telangiectasia.
They are associated with limited cutaneous systemic sclerosis and the CREST (calcinosis, Raynaud's syndrome, esophageal dysmotility, sclerodactyly, telangiectasia) variant.
A 53-year-old Caucasian male with a history of heavy alcohol use, first presented in September 2000 with a 1-year history of sclerodactyly and Raynaud's phenomenon.