protoporphyria /pro·to·por·phyr·ia/ (prōt″o-por-fēr´e-ah) erythropoietic p.
protoporphyria
erythropoietic protoporphyria (EPP) a form of erythropoietic porphyria marked by excessive protoporphyrin in erythrocytes, plasma, liver, and feces, and by widely varying photosensitive skin changes ranging from a burning or pruritic sensation to erythema, plaquelike edema, and wheals.
pro·to·por·phyr·i·a (pr  t-pôr-fîr  - )n. Enhanced fecal excretion of protoporphyrin. |
protoporphyria
[prō′tōpôrfir′ē·ə]
Etymology: Gk, protos + porphyros, purple, haima, blood
increased levels of protoporphyrin in the blood and feces.
protoporphyria
porphyria marked by excessive protoporphyrin in the erythrocytes, plasma and feces. The excess is due to a deficiency of the enzyme ferrochelatase and an increased formation of the protoporphyrin. The disease occurs in cattle and is similar to congenital erythropoietic porphyria but less severe with the only clinical abnormality being photosensitive dermatitis. The defect is inherited as a dominant trait.
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