proteinosis


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Related to proteinosis: lipoid proteinosis

proteinosis

 [pro″tēn-o´sis]
the accumulation of excess protein in the tissues.
alveolar proteinosis pulmonary alveolar proteinosis.
lipid proteinosis a hereditary defect of lipid metabolism marked by yellowish deposits of hyaline lipid carbohydrate mixture on the inner surface of the lips, under the tongue, and on the oropharynx and larynx, and in skin lesions.
pulmonary alveolar proteinosis see pulmonary alveolar proteinosis.

pro·tein·o·sis

(pro-tēn-ō'sis, prō'tē-in-ō'sis),
A state characterized by disordered protein formation and distribution, particularly as manifested by the deposition of abnormal proteins in tissues.
[protein + G. -osis, condition]

proteinosis

/pro·tein·o·sis/ (pro″tēn-o´sis) the accumulation of excess protein in the tissues.
lipid proteinosis  a hereditary defect of lipid metabolism marked by yellowish deposits of hyaline lipid-carbohydrate mixture on the inner surface of the lips, under the tongue, on the oropharynx, and on the larynx, and by skin lesions.
pulmonary alveolar proteinosis  a chronic lung disease in which the distal alveoli become filled with eosinophilic, probably endogenous proteinaceous material that prevents ventilation of affected areas.

pro·tein·o·sis

(prō'tē-nō'sis)
A state characterized by disordered protein formation and distribution, particularly as manifested by the deposition of abnormal proteins in tissues.
[protein + G. -osis, condition]

pro·tein·o·sis

(prō'tē-nō'sis)
A state characterized by disordered protein formation and distribution, particularly as manifested by deposition of abnormal proteins in tissues.
[protein+ G. -osis, condition]

proteinosis

the accumulation of excess protein in the tissues.
References in periodicals archive ?
Clinical and molecular study of the extracellular matrix protein 1 gene in a spanish family with lipoid proteinosis.
BOOP 02 Foreign body aspiration 01 Metastasis 02 Acute Myeloid Leukaemia 01 Pulmonary Alveolar 01 Pulmonary infarction 01 Proteinosis Strongyloides 01 Systemic Lupus 01 Erythematosus (SLE) Amiodarone 01 ILD 02 pneumonitis Wegener's 01 Middle lobe syndrome 01 granulomatosis Fungal pneumonia 01 Undiagnosed 03 Table 2: Sputum Examination Results Sputum Examination Number of +ve Result Acid Fast Bacilli (AFB) Culture 14 Other bacteria in culture 10 Fungal Culture 06 Sputum cytology for Malignant cells 11 Strongyloides.
Lipoid proteinosis maps to 1q21 and is caused by mutations in the extracellular matrix protein 1 gene (ECM1).
Nakata, "Pulmonary alveolar proteinosis," The New England Journal of Medicine, vol.
Clinical and molecular characterization of lipoid proteinosis in Namaqualand, South Africa.
are only few reports regarding lipoid proteinosis in literature and in this part of the world.
Familial CFA/IPF) CPI DLPD related with known causes (for example: drug, aspiration, Other interstitial connective tissue penumonia forms diseases, infections, environement) Hypersensitivity pneumonia LAM Interstitial pneumonia types LCG (NSIP, DIP, LIP, UIP, DAD, CP) Alveolar proteinosis Sarcoidosis Eosinophilic pneumonia Idiopatic/infantile pulmonary hemosiderosis Persistent tachypnea of infancy Pulmonary interstitial glycogenosis DLPD related with known causes (for example: drug, aspiration, Congenital disorders connective tissue diseases, infections, environement) DIP Hypersensitivity pneumonia (DMB) Interstitial pneumonia types LIP (NSIP, DIP, LIP, UIP, DAD, CP) (IYS) Lipoid pneumonia (CMD) ?
There are several diffuse lung diseases with pulmonary calcifications which might be included in the differential diagnosis of PAM such as pulmonary alveolar proteinosis, amyloidosis, metastatic pulmonary calcification, pulmonary vascular diseases, hyperparathyroidism, previous DNA virus infection, and chronic renal failure.
Su correlato histologico es proteinosis alveolar pulmonar y son frecuentes las infecciones sobreagregadas por micobacterias.
The text opens with an historical overview, followed by physiological and radiological features of common ILDs, such as idiopathic interstitial pneumonia, non-specific interstitial pneumonitis, and sarcoidosis, and uncommon ILDs, such as lymphangioleiomyomatosis, Langerhans cell granulomatosis, drug-induced lung disease, eosinophilic lung disease, alveolar proteinosis, and alveolar michrolithiasis.
Winchester syndrome (OMIM 277950), systemic fibromatosis (OMIM 228550), stiff skin syndrome (OMIM 184900), lipoid proteinosis (OMIM 247100), and storage diseases including mucopolysacharoses, sphingolipidoses and mucilipidoses [Osterby et al.
Silicoproteinosis de patron alveolar difuso, similar a la proteinosis alveolar