proteinosis


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Related to proteinosis: lipoid proteinosis

proteinosis

 [pro″tēn-o´sis]
the accumulation of excess protein in the tissues.
alveolar proteinosis pulmonary alveolar proteinosis.
lipid proteinosis a hereditary defect of lipid metabolism marked by yellowish deposits of hyaline lipid carbohydrate mixture on the inner surface of the lips, under the tongue, and on the oropharynx and larynx, and in skin lesions.
pulmonary alveolar proteinosis see pulmonary alveolar proteinosis.

pro·tein·o·sis

(pro-tēn-ō'sis, prō'tē-in-ō'sis),
A state characterized by disordered protein formation and distribution, particularly as manifested by the deposition of abnormal proteins in tissues.
[protein + G. -osis, condition]

proteinosis

/pro·tein·o·sis/ (pro″tēn-o´sis) the accumulation of excess protein in the tissues.
lipid proteinosis  a hereditary defect of lipid metabolism marked by yellowish deposits of hyaline lipid-carbohydrate mixture on the inner surface of the lips, under the tongue, on the oropharynx, and on the larynx, and by skin lesions.
pulmonary alveolar proteinosis  a chronic lung disease in which the distal alveoli become filled with eosinophilic, probably endogenous proteinaceous material that prevents ventilation of affected areas.

pro·tein·o·sis

(prō'tē-nō'sis)
A state characterized by disordered protein formation and distribution, particularly as manifested by the deposition of abnormal proteins in tissues.
[protein + G. -osis, condition]

pro·tein·o·sis

(prō'tē-nō'sis)
A state characterized by disordered protein formation and distribution, particularly as manifested by deposition of abnormal proteins in tissues.
[protein+ G. -osis, condition]

proteinosis

the accumulation of excess protein in the tissues.
References in periodicals archive ?
Vascular anomalies in lipoid proteinosis (hyalinosis cubs et mucosael: Basement membrane components and ultrastrudure.
Idiopathic pulmonary alveolar proteinosis as an autoimmune disease with neutralizing antibody against granulocyte/macrophage colony-stimulating factor.
Lipoid proteinosis, which is also known in the literature as Urbach- Wiethe disease and hyalinosis cutis et mucosae, is a rare autosomal-recessive anomaly that primarily affects children.
7) On HRCT, lipoid pneumonia may show crazy-paving, a colorful description of patchy interlobular and intralobular septal thickening and ground-glass opacity that may also be seen with other diseases, including pulmonary alveolar proteinosis, lung edema, Pneumocystis jiroveci pneumonia, and bronchioloalveolar carcinoma.
Other research topics included specifically South African subjects, such as reconstructing the history of preliterate peoples of the subcontinent employing blood groups and protein characteristics, oculocutaneous albinism in the black population, TSD in Jewish people, pentosuria, cystic fibrosis, Fanconi's anaemia, fragile X syndrome, the Y chromosome, mitochondrial DNA, haemoglobin variation (haemoglobinopathies) and disorders in the black and Indian populations, keratolytic winter erythema, lipoid proteinosis, intellectual disability, fetal alcohol syndrome, and other rarer conditions.
Cases of NSIP with evidence of desquamative interstitial pneumonia-like change and foci intra-alveolar proteinosis should be examined by electron microscopy, immunohistochemistry, and genetic testing to exclude an adult form of congenital surfactant protein deficiency.
Two other diseases of interest as differential diagnoses of vocal fold deposits are amyloidosis and lipoid proteinosis (Urbach-Wiethe's disease):
42) Recurrence of the primary disease has been described with many conditions, including sarcoidosis, lymphangioleiomyomatosis, Langerhans cell histiocytosis, talc granulomatosis, diffuse panbronchiolitis, and alveolar proteinosis.
Urschel and Campbell reported on several new procedures for surgery of the trachea: tracheal splints; total replacement of the trachea and lower larynx, including the vocal cords with Silastic stents; and bronchopulmonary lavage for pulmonary alveolar proteinosis.
Elevated levels of lung surfactant protein A in sera from patients with idiopathic pulmonary fibrosis and pulmonary alveolar proteinosis.
Lipoid proteinosis (Urbach-Wiethe disease, hyalinosis cutis et mucosae) is an autosomal-recessive condition with variable penetrance.
Pulmonary alveolar proteinosis is a rare disease of the lung in which excessive thick granular phospholipoproteinaceous material accumulates within the air spaces.