primary amyloidosis


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Related to primary amyloidosis: secondary amyloidosis, familial amyloidosis

pri·mar·y am·y·loi·do·sis

several forms of amyloidosis are known, following autosomal dominant [MIM *104750, *105120, *105150, *105200, *105210, *105250] recessive [MIM 204850 and *204900], and X-linked [MIM 301220] inheritance and not associated with other recognized disease. Tends to involve diffusely the arterial walls and mesenchymal tissues in the tongue, lungs, intestinal tract, skin, skeletal muscle, and myocardium, interfering with vital functions; the amyloid frequently does not manifest the usual affinity for Congo red stain, and sometimes provokes a foreign-body type of inflammatory reaction in the adjacent tissue.

primary amyloidosis

pri·mar·y a·my·loid·o·sis

(prī'mar-ē am'i-loy-dō'sis)
Amyloidosis not associated with other recognized disease; tends to involve arterial walls and mesenchymal tissues in the tongue, lungs, intestinal tract, skin, skeletal muscle, and myocardium; the amyloid frequently does not manifest the usual affinity for Congo red and sometimes provokes a foreign-body type of inflammatory reaction.

pri·mar·y a·my·loid·o·sis

(prī'mar-ē am'i-loy-dō'sis)
Form of the disorder not associated with other recognized disease; tends to involve arterial walls and mesenchymal tissues in the tongue, lungs, intestinal tract, skin, skeletal muscle, and myocardium.

Patient discussion about primary amyloidosis

Q. How fast can primary amyloidosis spread? And what is the average survival rate for this disease?

A. Your best bet for one-stop shopping for amyloidosis information on the net is http://www.amyloidosis.org. There is also a Yahoo group named amyloidosis and also a mailing list named amyloid hosted by the Association of Cancer Online Resources. The amyloid list has around 500 subscribers, amyloidosis Yahoo group has maybe half that many. Face-to-face support for patients and caregivers is also available in most large metropolitan areas two or three times a year. See http://www.amyloidosissupportgroups.com for details.

To join the amyloid list, see http://www.acor.org/amyloid.html

More discussions about primary amyloidosis
References in periodicals archive ?
Presentation and course of primary amyloidosis of the kidney.
Our patient had primary amyloidosis with renal, cardiac and hepatic involvement.
Cardiac involvement is both more severe and more frequent in patients with primary amyloidosis, and is invariably fatal.
A tongue resection in macroglossia due to primary amyloidosis.
The clinical application of serum free light chain measurements was particularly apparent for detecting and monitoring patients with nonsecretory myeloma and primary amyloidosis.
Detection of serum immunoglobulin free light chains in primary amyloidosis and light chain deposition disease by nephelometry [Abstract].
We used urine samples obtained from inpatients with multiple myeloma (n = 9), benign monoclonal gammopathy (n = 1), primary macroglobulinemia (n = 1), light chain deposition disease (n = 1), and primary amyloidosis (n = 5).

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