At CT/MRI, cystic nephroma
presents as a well-circumscribed, multilocular cystic mass with multiple minimally thickened septations that enhance on contrast administration; cystic spaces may contain simple or hemorrhagic fluid.
in an adult patient: recurrence 21 years after removal of the primary lesion.
1,2] The ossification and mesenchymal components are similar to mesoblastic nephroma
is entirely cystic, without any solid expansile growth or mural nodules.
in adults is considered to belong to the spectrum of cystic renal lesions, ranging from typical cystic nephroma
to mixed epithelial and stromal tumor of the kidney.
ETV6-NTRK3 gene fusions and trisomy 11 establish a histogenetic link between mesoblastic nephroma
and congenital fibrosarcoma.
Other possible diagnoses for antenatal suprarenal cysts include benign entities, such as adrenal hemorrhage, retropleural pulmonary sequestration, neurogenic cysts, enteric duplication cysts and malignant diseases, including Wilm's tumour and congenital mesoblastic nephroma
2,52-54) In 25% to 30% of cases, PPB is a part of a hereditary tumor syndrome that includes cystic nephroma
, rhabdomyosarcoma, and Wilms tumor.
Multilocular renal cysts-cystic nephroma
and congeners 11.
59,60) Hyperechogenic unilateral or bilateral changes detected in prenatal or postnatal screening raise a long differential diagnosis, including ARPKD, early-onset ADPKD, multicystic renal dysplasia, congenital nephrotic syndrome, cystic nephroma
, and renal vein thrombosis.
3-11) These tumors have been published under the following names in the literature: leiomyomatous renal hamartomas, congenital mesoblastic nephroma
in an adult, cystic hamartoma of renal pelvis, solitary multilocular cysts of the kidney, multilocular renal cyst with mullerian-like stroma, and adult metanephric stromal tumor.
2) Other renal tumors of childhood have been associated with recurring genetic abnormalities: deletion or mutations of WT1 and p53 in some Wilms tumors, t (12;15) creating the ETV6-NTRK3 fusion gene in congenital mesoblastic nephroma
, and INI1 deletions or mutations in malignant rhabdoid tumors.