neonatal hemochromatosis


Also found in: Dictionary, Thesaurus, Financial, Encyclopedia, Wikipedia.

neonatal hemochromatosis

Metabolic disease A fulminant disease characterized by massive hepatic iron loading and perinatal liver failure, accompanied by myocardial and pancreatic acinar iron overload Management Liver transplant–rarely successful. Cf Hemochromatosis, Juvenile hemochromatosis.

neonatal hemochromatosis

,

NH

A rare congenital disorder causing iron overload in the fetus and newborn, resulting in intrauterine growth retardation, premature birth, end-stage liver disease at birth, or intrauterine death.
Mentioned in ?