myoclonic astatic epilepsy

my·o·clon·ic a·stat·ic ep·i·lep·sy

a petit mal variant characterized by atonic (drop attacks) and tonic or tonic-clonic attacks in neurologically disabled for example, hemiplegic, ataxic children with mental retardation; characterized in EEG by 2-second spike and wave discharges; usually progresses in spite of medication.

my·o·clon·ic a·stat·ic ep·i·lep·sy

(MAE) (mī'ō-klon'ik ā-stat'ik ep'i-lep'sē)
A cryptogenic variant characterized by atonic (drop attacks) and tonic or tonic-clonic attacks in neurologically disabled children (e.g., patients with hemiplegia, ataxia) with mental retardation; usually progresses despite medication.
References in periodicals archive ?
Myoclonic astatic epilepsy starts in previously healthy children aged 2-5 years old with repeating generalized tonic-clonic seizures accompanied by diffuse spike-sharp wave activity on EEG.
Doctors in August 2006 diagnosed Alex with a severe form of epilepsy called Myoclonic Astatic Epilepsy, also known as Doose Syndrome.
Undefined SGE was present in 28 (37%), 32 (43%) had West's syndrome, 4 (5%) had Lennox-Gastaut syndrome, and 9 (12%) had myoclonic astatic epilepsy.