lipofuscinosis /lipo·fus·cin·o·sis/ (-fu″sin-o´sis) any disorder due to abnormal storage of lipofuscins.
lipofuscinosis [lip″o-fu″sin-o´sis]
neuronal ceroid-lipofuscinosis any of several genetic lipidoses characterized by progressive neurodegeneration, loss of vision, and a fatal course; included are Janský-Bielschowsky disease, Vogt-Spielmeyer disease, and Kufs' disease.
lip·o·fus·ci·no·sis (l p  -f s -n ss, -fy s-)n. Abnormal storage of any one of a group of fatty pigments. |
lipofuscinosis [lip″o-fu″sin-o´sis]
any disorder due to abnormal storage of lipofuscins.
neuronal ceroid-lipofuscinosis any of several genetic lipidoses characterized by progressive neurodegeneration, loss of vision, and a fatal course; included are janský-bielschowsky disease, vogt-spielmeyer disease, and kufs' disease. Formerly known as amaurotic familial idiocy.
lipofuscinosis
any disorder due to abnormal storage of lipofuscins.
ceroid lipofuscinosis
an inherited disease in sheep, cattle, dogs and cats, characterized by blindness, mental dullness and abnormal behavior. There is atrophy of the brain with extensive accumulation of lipopigments ('ceroid bodies') in nervous tissue and later viscera as well. The comparable, though possibly not identical, disease in humans is also called Batten disease.
hepatic lipofuscinosis
a deposit of lipofuscin in partly oxidized form in the livers of sheep, which gives them a deep black color and makes them unsaleable. The condition is common in areas where the mulga tree (Acacia aneura) grows and the leaves are fed to sheep as fodder.
Want to thank TFD for its existence? Tell a friend about us, add a link to this page, add the site to iGoogle, or visit the webmaster's page for free fun content.
| ?Page tools | ||
|---|---|---|
|