lamellar ichthyosis

ichthyosis /ich·thy·o·sis/ (-sis) any in a group of cutaneous disorders characterized by increased or aberrant keratinization, resulting in noninflammatory scaling of the skin; most are genetically determined; often used to denote i. vulgaris. ichthyot´ic

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ichthyosis hys´trix  a rare form of epidermolytic hyperkeratosis, marked by generalized, dark brown, linear verrucoid ridges somewhat like porcupine skin.

lamellar ichthyosis  a hereditary disease present at or soon after birth, with large, quadrilateral, grayish brown scales; it may be associated with short stature, oligophrenia, spastic paralysis, genital hypoplasia, hypotrichia, and shortened life-span.

ichthyosis sim´plex  i. vulgaris.

ichthyosis u´teri  transformation of the columnar epithelium of the endometrium into stratified squamous epithelium.

ichthyosis vulga´ris  hereditary ichthyosis present at or shortly after birth, with large, thick, dry scales on the neck, ears, scalp, face, and flexural surfaces.

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lamellar ichthyosis

n.

An inherited form of ichthyosis that is present at birth and is characterized by large, coarse scales over most of the body and thickened palms and soles; it is associated with ectropion.

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Lamellar ichthyosis

Also called fish scale disease, this inherited condition is characterized by darkened, scaly, dry patches of skin.

Mentioned in: Skin Pigmentation Disorders

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lamellar ichthyosis

Collodion baby, nonbullous congenital ichthyosiform erythroderma Dermatology An AR condition characterized by a brittle shell-like skin surface in infancy, which gives rise to coarse scaling of the skin surface, especially on flexures of extremities. See Ichthyosis.