incontinentia pigmenti

incontinentia /in·con·ti·nen·tia/ (-kon″tĭ-nen´shah) [L.] incontinence.

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incontinentia pigmen´ti  a hereditary disorder in which early vesicular and later verrucous and bizarrely pigmented skin lesions are associated with eye, bone, and central nervous system defects.

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in·con·ti·nen·tia pig·men·ti (n-knt-nnsh pg-mnt)

n.

An inherited developmental defect of the skin marked by pigmented lesions in linear, zebra-stripe, and other configurations and often involving other structures such as the central nervous system. Also called Bloch-Sulzberger syndrome.

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incontinentia pigmenti

[inkon′tinen′shə pigmen′tī]

a male-lethal X-linked dominant syndrome with onset at birth or shortly thereafter, characterized by the presence of brown or slate-brown bands, whorls, swirls, or splatter-like hyperpigmented cutaneous lesions, preceded by vesiculobullous and verrucous inflammatory changes, often associated with developmental anomalies involving other structures, such as the hair, eyes, and skeletal and central nervous systems. Also called Bloch-Sulzberger incontinentia pigmenti, Bloch-Sulzberger syndrome.

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incontinentia pigmenti,

n See syndrome, Bloch-Sulzberger.