idiopathic pulmonary hemosiderosis

idiopathic pulmonary hemosiderosis

n.

Repeated attacks of difficulty in breathing and hemoptysis leading to the deposition of abnormal amounts of hemosiderin in the lungs. Also called Ceelen-Gellerstadt syndrome.

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idiopathic pulmonary hemosiderosis

Clinical immunology A rare possibly autoimmune condition affecting children < age 10 characterized by hemosiderin deposition in lungs Clinical Recurrent hemoptysis, anemia, weakness, clubbing, hepatosplenomegaly Prognosis Poor, recurrent episodes; death often in 5 yrs due to cor pulmonale; it may be associated with celiac disease and improve with a gluten-free diet. See Hemosiderosis.