hypoplastic left heart syndrome

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hypoplastic left heart syndrome

congenital hypoplasia or atresia of the left ventricle, the aortic or mitral valve, and the ascending aorta, with respiratory distress, cardiac failure, and death in infancy.

hy·po·plas·tic left heart syn·drome

association of underdevelopment of the left heart chambers with atresia or stenosis of the aortic and/or mitral valve and hypoplasia of the ascending aorta.

hypoplastic left heart syndrome (HLHS)

any of a group of congenital anomalies consisting of hypoplasia or atresia of the left ventricle and of the aortic or mitral valve or both and hypoplasia of the ascending aorta. It is characterized by respiratory distress and extreme cyanosis, with cardiac failure and death in early infancy.

hypoplastic left heart syndrome

Pediatric cardiology A group of congenital often AR cardiac defects characterized by hypo- or agenesis of the left ventricle, aortic and mitral valves, an atrial right-to-left shunt; right-sided hypoplasia of tricuspid or pulmonary valves, pulmonary stenosis, or right ventricular hypoplasia; the ascending and transverse aorta is narrowed with a diaphragm-like aortic coarctation at the preductal aortic isthmus; postnatal life hinges on adequate blood supply–ie, is ductus dependent, unrestricted atrial shunting, and a balance between the pulmonary and systemic vascular resistances; surgery is difficult as there are extensive malformations Mortality High. See Baby Fae heart.


characterized by hypoplasia, e.g. hypoplastic anemia.

hypoplastic left heart syndrome
a congenital anomaly seen in cats in which there is mitral atresia and incomplete development of the left ventricle and aortic valve.
References in periodicals archive ?
Survival analysis and risk factors for mortality in transplantation and staged surgery in hypoplastic left heart syndrome.
Parents Michael and Diane McIntyre have spent the last 11 weeks at the Freeman Hospital as their son Dante-Alexander was born with the rare defect hypoplastic left heart syndrome - a complex condition that affects only one in every 5,000 babies.
Washington, November 7 ( ANI ): Surgeons including one of Indian origin at Boston Children's Hospital have established a new approach for rebuilding the heart in children born with a severe heart defect called hypoplastic left heart syndrome (HLHS).
Born with Hypoplastic Left Heart Syndrome, Lara has only half a functioning heart.
Kylie discovered her third child Preston had hypoplastic left heart syndrome - a condition where one side of the heart is severely underdeveloped - during her routine 20-week scan.
Mum, Tracy Morris, said the condition, hypoplastic left heart syndrome, was diagnosed within 24 hours of Liberty's birth at Ysbyty Glan Clwyd, Bodelwyddan and she was transferred to Liverpool's Alder Hey children's hospital.
We know other kids with hypoplastic left heart syndrome, and they're doing well, so we're hoping this is just a bump in the road.
Fetuses with hypoplastic left heart syndrome and normal chromosomes are unlikely to die in utero, according to a retrospective study of 176 fetuses diagnosed prenatally with the disorder.
He was diagnosed with hypoplastic left heart syndrome two days after birth and transferred straight to the Children's, which is one of five major heart centres in the UK.
Hypoplastic Left Heart Syndrome (HLHS) is one of the most complex congenital heart defects.